常染色体显性多囊肾病的诊断、监测及治疗
<正>常染色体显性多囊肾病(ADPKD)患病率约为1‰<sup>2</sup>‰,是最常见的遗传性肾病<sup>[1]</sup>。ADPKD是西方导致终末期肾病(ESRD)的第4大病因,约占透析人数的5%<sup>1</sup>0%,约半数ADPKD患者于60岁前进入ESRD,主要依靠肾脏替代治疗维持生命<sup>[2]</sup>。我国约有150万例ADPKD患者<sup>[3]</sup>。ADPKD致病基因主要有两个,PKD1和PKD2。...
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| Main Authors: | , , , |
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| Format: | Article |
| Language: | zho |
| Published: |
Editorial Department of Journal of Clinical Nephrology
2018-01-01
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| Series: | Linchuang shenzangbing zazhi |
| Online Access: | http://www.lcszb.com/thesisDetails?columnId=57917254&Fpath=home&index=0 |
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