Impaired platelet function in Hermansky-Pudlak syndrome associated with novel mutations in <i>HPS3</i>, <i>HPS6</i> and <i>HPS8</i> genes

We report three unrelated cases of Hermansky-Pudlak (HP) characterized by novel mutations in HPS3 (compound heterozygosity for c.1457G>A and c.1813G>T), HPS6 (homozygous c.210_211insGGGCC), and HPS8 (homozygous c.299dupC in BLOC1S3) genes. No spontaneous bleeding tendency was observed despite...

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Bibliographic Details
Main Authors: Lisa Pieri, Silvia Linari, Francesca Salvianti, Monica Attanasio, Giancarlo Castaman
Format: Article
Language:English
Published: PAGEPress Publications 2024-11-01
Series:Bleeding, Thrombosis and Vascular Biology
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Online Access:https://www.btvb.org/btvb/article/view/150
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