Scoliosis in Shprintzen–Goldberg Syndrome
We report a case of scoliosis in a 12-year-old girl with Shprintzen–Goldberg syndrome. She was diagnosed with Shprintzen–Goldberg syndrome at birth. She was hospitalized for a surgical treatment because scoliosis gradually progressed. Preoperative X-ray confirmed 80° symptomatic scoliosis in T10–L5....
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Format: | Article |
Language: | English |
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Wiley
2020-01-01
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Series: | Case Reports in Orthopedics |
Online Access: | http://dx.doi.org/10.1155/2020/8857463 |
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author | Hiromitsu Takano Ikuho Yonezawa Takatoshi Okuda Hajime Kajihara Kazuo Kaneko |
author_facet | Hiromitsu Takano Ikuho Yonezawa Takatoshi Okuda Hajime Kajihara Kazuo Kaneko |
author_sort | Hiromitsu Takano |
collection | DOAJ |
description | We report a case of scoliosis in a 12-year-old girl with Shprintzen–Goldberg syndrome. She was diagnosed with Shprintzen–Goldberg syndrome at birth. She was hospitalized for a surgical treatment because scoliosis gradually progressed. Preoperative X-ray confirmed 80° symptomatic scoliosis in T10–L5. Posterior correction and fusion were performed, and postoperative X-ray showed a correction to 43°in T10-L5. Limited subcutaneous tissues and fragile bones must be considered when selecting the appropriate surgical method. Accurate placement of a screw into thin pedicle is essential to obtain sufficient correction and fusion. The use of a navigation system is recommended. |
format | Article |
id | doaj-art-fb5796446ea1412f826eaa00a0fbd2e3 |
institution | Kabale University |
issn | 2090-6749 2090-6757 |
language | English |
publishDate | 2020-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Orthopedics |
spelling | doaj-art-fb5796446ea1412f826eaa00a0fbd2e32025-02-03T06:05:39ZengWileyCase Reports in Orthopedics2090-67492090-67572020-01-01202010.1155/2020/88574638857463Scoliosis in Shprintzen–Goldberg SyndromeHiromitsu Takano0Ikuho Yonezawa1Takatoshi Okuda2Hajime Kajihara3Kazuo Kaneko4Department of Orthopedic Surgery, Koto Hospital, 6-8-5 Ojima, Koto-ku, Tokyo 136-0072, JapanDepartment of Orthopedic Surgery, Juntendo University School of Medicine, 2-1-1 Hongo, Bunkyo-ku, Tokyo 113-8421, JapanDepartment of Orthopedic Surgery, Juntendo University School of Medicine, 2-1-1 Hongo, Bunkyo-ku, Tokyo 113-8421, JapanDepartment of Orthopedic Surgery, Koto Hospital, 6-8-5 Ojima, Koto-ku, Tokyo 136-0072, JapanDepartment of Orthopedic Surgery, Juntendo University School of Medicine, 2-1-1 Hongo, Bunkyo-ku, Tokyo 113-8421, JapanWe report a case of scoliosis in a 12-year-old girl with Shprintzen–Goldberg syndrome. She was diagnosed with Shprintzen–Goldberg syndrome at birth. She was hospitalized for a surgical treatment because scoliosis gradually progressed. Preoperative X-ray confirmed 80° symptomatic scoliosis in T10–L5. Posterior correction and fusion were performed, and postoperative X-ray showed a correction to 43°in T10-L5. Limited subcutaneous tissues and fragile bones must be considered when selecting the appropriate surgical method. Accurate placement of a screw into thin pedicle is essential to obtain sufficient correction and fusion. The use of a navigation system is recommended.http://dx.doi.org/10.1155/2020/8857463 |
spellingShingle | Hiromitsu Takano Ikuho Yonezawa Takatoshi Okuda Hajime Kajihara Kazuo Kaneko Scoliosis in Shprintzen–Goldberg Syndrome Case Reports in Orthopedics |
title | Scoliosis in Shprintzen–Goldberg Syndrome |
title_full | Scoliosis in Shprintzen–Goldberg Syndrome |
title_fullStr | Scoliosis in Shprintzen–Goldberg Syndrome |
title_full_unstemmed | Scoliosis in Shprintzen–Goldberg Syndrome |
title_short | Scoliosis in Shprintzen–Goldberg Syndrome |
title_sort | scoliosis in shprintzen goldberg syndrome |
url | http://dx.doi.org/10.1155/2020/8857463 |
work_keys_str_mv | AT hiromitsutakano scoliosisinshprintzengoldbergsyndrome AT ikuhoyonezawa scoliosisinshprintzengoldbergsyndrome AT takatoshiokuda scoliosisinshprintzengoldbergsyndrome AT hajimekajihara scoliosisinshprintzengoldbergsyndrome AT kazuokaneko scoliosisinshprintzengoldbergsyndrome |