A rare cause of hepatomegaly and dyslipidemia: lysosomal acid lipase deficiency

Background. Lysosomal acid lipase deficiency (LAL-D), also known as cholesteryl ester storage disease or Wolman disease, is a multi-systemic autosomal recessive genetic disorder caused by mutations in the lysosomal acid lipase gene (LIPA). Case. A 14-year-old female patient was diagnos...

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Bibliographic Details
Main Authors: Berrak Bilginer Gürbüz, İlker Güney, Fatma Derya Bulut, Okan Dilek
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2020-10-01
Series:The Turkish Journal of Pediatrics
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Online Access:https://turkjpediatr.org/article/view/520
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