Heterodimerization of Two Pathological Mutants Enhances the Activity of Human Phosphomannomutase2.

The most frequent disorder of glycosylation is due to mutations in the gene encoding phosphomannomutase2 (PMM2-CDG). For this disease, which is autosomal and recessive, there is no cure at present. Most patients are composite heterozygous and carry one allele encoding an inactive mutant, R141H, and...

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Bibliographic Details
Main Authors: Giuseppina Andreotti, Maria Chiara Monti, Valentina Citro, Maria Vittoria Cubellis
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2015-01-01
Series:PLoS ONE
Online Access:https://doi.org/10.1371/journal.pone.0139882
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