Synchrotron‐Based Phase‐Contrast Micro‐CT Combined With Histology to Decipher Differences Between Hereditary and Sporadic Pediatric Pulmonary Veno‐Occlusive Disease

Synchrotron‐Based Phase‐Contrast Micro‐CT Combined With Histology to Decipher Differences Between Hereditary and Sporadic Pediatric Pulmonary Veno‐Occlusive Disease

ABSTRACT Pulmonary veno‐occlusive disease (PVOD) is a lethal variant of pulmonary hypertension. The degree of pulmonary arterial involvement varies. Here, we compare two PVOD patients who were transplanted at 8 years of age, whereof one is a homozygous EIF2AK4 mutation carrier. Tissue was imaged wit...

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Main Authors: Ida Jeremiasen, Niccolò Peruzzi, Elna Lampei, Sofie Meyer, Levent M. Akyürek, Erik Gebre‐Medhin, Ceren Mutgan, Peter Dorfmüller, Lavinia Neubert, Danny Jonigk, Csaba Galambos, Karin Tran‐Lundmark
Format: Article
Language:English
Published: Wiley 2024-10-01
Series:Pulmonary Circulation
Subjects:
children
EIF2AK4 mutation
pulmonary hypertension
pulmonary veno‐occlusive disease
synchrotron
Online Access:https://doi.org/10.1002/pul2.70024
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https://doi.org/10.1002/pul2.70024

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