Bullous skin lesions in a jaundiced infant after phototherapy: a case of congenital erythropoietic porphyria

Congenital erythropoietic porphyria is a rare autosomal recessive disorder of porphyrin metabolism in which the genetic defect is the deficiency of uroporphyrinogen III cosynthase (UIIIC). Deficiency of this enzyme results in an accumulation of high amounts of uroporphyrin I in all tissues, l...

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Bibliographic Details
Main Authors: Maşallah Baran, Kayı Eliaçık, Ismail Kurt, Ali Kanık, Neslihan Zengin, Ali Rahmi Bakiler
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2013-04-01
Series:The Turkish Journal of Pediatrics
Online Access:https://turkjpediatr.org/article/view/1485
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