Importance of neurologic and cutaneous signs in the diagnosis of Schimke immuno-osseous dysplasia

Schimke immuno-osseous dysplasia is an autosomal recessive multisystem disorder caused by defects in SWI/SNF-related, matrix-associated, actin-dependent regulator of chromatin, subfamily a-like 1 gene (SMARCAL1). SMARCAL1 product is a helicase that has role in selective cellular proliferation...

Full description

Saved in:
Bibliographic Details
Main Authors: Ayşe İpek Polat, Uluç Yiş, Müge Ayanoğlu, Ayşe Semra Hız, Handan Güleryüz, Tülay Öztürk Atasoy, Cornelius F Boerkoel
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2015-10-01
Series:The Turkish Journal of Pediatrics
Online Access:https://turkjpediatr.org/article/view/1276
Tags: Add Tag
No Tags, Be the first to tag this record!