Pediatric antineutrophil cytoplasmic antibody-associated vasculitis: A review on pulmonary manifestations, management, and outcomes

Antineutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) is a rare systemic autoimmune disorder characterized by necrotizing inflammation of blood vessels infiltrated by neutrophils. It includes three distinct entities: granulomatosis with polyangiitis (GPA, formerly known as Wegener’s g...

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Bibliographic Details
Main Authors: Chien-Heng Lin, Chieh-Ho Chen, Wei-Ching Lin, Wen-Jue Soong, Syuan-Yu Hong
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-09-01
Series:Tungs’ Medical Journal
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Online Access:https://journals.lww.com/tmj/fulltext/2024/09001/pediatric_antineutrophil_cytoplasmic.3.aspx
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