Pediatric antineutrophil cytoplasmic antibody-associated vasculitis: A review on pulmonary manifestations, management, and outcomes
Antineutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) is a rare systemic autoimmune disorder characterized by necrotizing inflammation of blood vessels infiltrated by neutrophils. It includes three distinct entities: granulomatosis with polyangiitis (GPA, formerly known as Wegener’s g...
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| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2024-09-01
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| Series: | Tungs’ Medical Journal |
| Subjects: | |
| Online Access: | https://journals.lww.com/tmj/fulltext/2024/09001/pediatric_antineutrophil_cytoplasmic.3.aspx |
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