Missense variants in FRS3 affect body mass index in populations of diverse ancestries

Abstract Obesity is associated with adverse effects on health and quality of life. Improved understanding of its underlying pathophysiology is essential for developing counteractive measures. To search for sequence variants with large effects on BMI, we perform a multi-ancestry meta-analysis of 13 g...

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Main Authors: Andrea B. Jonsdottir, Gardar Sveinbjornsson, Rosa B. Thorolfsdottir, Max Tamlander, Vinicius Tragante, Thorhildur Olafsdottir, Solvi Rognvaldsson, Asgeir Sigurdsson, Hannes P. Eggertsson, Hildur M. Aegisdottir, David O. Arnar, Karina Banasik, Doruk Beyter, Ragnar G. Bjarnason, Gyda Bjornsdottir, Søren Brunak, Mie Topholm Bruun, Joseph Dowsett, Eythor Einarsson, Gudmundur Einarsson, Christian Erikstrup, Run Fridriksdottir, Jonas Ghouse, Solveig Gretarsdottir, Gisli H. Halldorsson, Torben Hansen, Anna Helgadottir, Peter C. Holm, Erna V. Ivarsdottir, Kasper Karmark Iversen, Bitten Aagaard Jensen, Ingileif Jonsdottir, Stacey Knight, Kirk U. Knowlton, Snaedis Kristmundsdottir, Adalheidur E. Larusdottir, Olafur Th. Magnusson, Gisli Masson, Pall Melsted, Christina Mikkelsen, Kristjan H. S. Moore, Asmundur Oddsson, Pall I. Olason, Frosti Palsson, Ole Birger Pedersen, Michael Schwinn, Emil L. Sigurdsson, Aron Skaftason, Lilja Stefansdottir, Hreinn Stefansson, Thora Steingrimsdottir, Arni Sturluson, Unnur Styrkarsdottir, Erik Sørensen, Unnur D. Teitsdottir, Thorgeir E. Thorgeirsson, Gudmundur A. Thorisson, Unnur Thorsteinsdottir, Magnus O. Ulfarsson, Henrik Ullum, Arnor Vikingsson, G. Bragi Walters, DBDS Genomic Consortium, Lincoln D. Nadauld, Henning Bundgaard, Sisse Rye Ostrowski, Agnar Helgason, Bjarni V. Halldorsson, Gudmundur L. Norddahl, Samuli Ripatti, Daniel F. Gudbjartsson, Gudmar Thorleifsson, Valgerdur Steinthorsdottir, Hilma Holm, Patrick Sulem, Kari Stefansson
Format: Article
Language:English
Published: Nature Portfolio 2025-03-01
Series:Nature Communications
Online Access:https://doi.org/10.1038/s41467-025-57753-2
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author Andrea B. Jonsdottir
Gardar Sveinbjornsson
Rosa B. Thorolfsdottir
Max Tamlander
Vinicius Tragante
Thorhildur Olafsdottir
Solvi Rognvaldsson
Asgeir Sigurdsson
Hannes P. Eggertsson
Hildur M. Aegisdottir
David O. Arnar
Karina Banasik
Doruk Beyter
Ragnar G. Bjarnason
Gyda Bjornsdottir
Søren Brunak
Mie Topholm Bruun
Joseph Dowsett
Eythor Einarsson
Gudmundur Einarsson
Christian Erikstrup
Run Fridriksdottir
Jonas Ghouse
Solveig Gretarsdottir
Gisli H. Halldorsson
Torben Hansen
Anna Helgadottir
Peter C. Holm
Erna V. Ivarsdottir
Kasper Karmark Iversen
Bitten Aagaard Jensen
Ingileif Jonsdottir
Stacey Knight
Kirk U. Knowlton
Snaedis Kristmundsdottir
Adalheidur E. Larusdottir
Olafur Th. Magnusson
Gisli Masson
Pall Melsted
Christina Mikkelsen
Kristjan H. S. Moore
Asmundur Oddsson
Pall I. Olason
Frosti Palsson
Ole Birger Pedersen
Michael Schwinn
Emil L. Sigurdsson
Aron Skaftason
Lilja Stefansdottir
Hreinn Stefansson
Thora Steingrimsdottir
Arni Sturluson
Unnur Styrkarsdottir
Erik Sørensen
Unnur D. Teitsdottir
Thorgeir E. Thorgeirsson
Gudmundur A. Thorisson
Unnur Thorsteinsdottir
Magnus O. Ulfarsson
Henrik Ullum
Arnor Vikingsson
G. Bragi Walters
DBDS Genomic Consortium
Lincoln D. Nadauld
Henning Bundgaard
Sisse Rye Ostrowski
Agnar Helgason
Bjarni V. Halldorsson
Gudmundur L. Norddahl
Samuli Ripatti
Daniel F. Gudbjartsson
Gudmar Thorleifsson
Valgerdur Steinthorsdottir
Hilma Holm
Patrick Sulem
Kari Stefansson
author_facet Andrea B. Jonsdottir
Gardar Sveinbjornsson
Rosa B. Thorolfsdottir
Max Tamlander
Vinicius Tragante
Thorhildur Olafsdottir
Solvi Rognvaldsson
Asgeir Sigurdsson
Hannes P. Eggertsson
Hildur M. Aegisdottir
David O. Arnar
Karina Banasik
Doruk Beyter
Ragnar G. Bjarnason
Gyda Bjornsdottir
Søren Brunak
Mie Topholm Bruun
Joseph Dowsett
Eythor Einarsson
Gudmundur Einarsson
Christian Erikstrup
Run Fridriksdottir
Jonas Ghouse
Solveig Gretarsdottir
Gisli H. Halldorsson
Torben Hansen
Anna Helgadottir
Peter C. Holm
Erna V. Ivarsdottir
Kasper Karmark Iversen
Bitten Aagaard Jensen
Ingileif Jonsdottir
Stacey Knight
Kirk U. Knowlton
Snaedis Kristmundsdottir
Adalheidur E. Larusdottir
Olafur Th. Magnusson
Gisli Masson
Pall Melsted
Christina Mikkelsen
Kristjan H. S. Moore
Asmundur Oddsson
Pall I. Olason
Frosti Palsson
Ole Birger Pedersen
Michael Schwinn
Emil L. Sigurdsson
Aron Skaftason
Lilja Stefansdottir
Hreinn Stefansson
Thora Steingrimsdottir
Arni Sturluson
Unnur Styrkarsdottir
Erik Sørensen
Unnur D. Teitsdottir
Thorgeir E. Thorgeirsson
Gudmundur A. Thorisson
Unnur Thorsteinsdottir
Magnus O. Ulfarsson
Henrik Ullum
Arnor Vikingsson
G. Bragi Walters
DBDS Genomic Consortium
Lincoln D. Nadauld
Henning Bundgaard
Sisse Rye Ostrowski
Agnar Helgason
Bjarni V. Halldorsson
Gudmundur L. Norddahl
Samuli Ripatti
Daniel F. Gudbjartsson
Gudmar Thorleifsson
Valgerdur Steinthorsdottir
Hilma Holm
Patrick Sulem
Kari Stefansson
author_sort Andrea B. Jonsdottir
collection DOAJ
description Abstract Obesity is associated with adverse effects on health and quality of life. Improved understanding of its underlying pathophysiology is essential for developing counteractive measures. To search for sequence variants with large effects on BMI, we perform a multi-ancestry meta-analysis of 13 genome-wide association studies on BMI, including data derived from 1,534,555 individuals of European ancestry, 339,657 of Asian ancestry, and 130,968 of African ancestry. We identify an intergenic 262,760 base pair deletion at the MC4R locus that associates with 4.11 kg/m2 higher BMI per allele, likely through downregulation of MC4R. Moreover, a rare FRS3 missense variant, p.Glu115Lys, only found in individuals from Finland, associates with 1.09 kg/m2 lower BMI per allele. We also detect three other low-frequency FRS3 missense variants that associate with BMI with smaller effects and are enriched in different ancestries. We characterize FRS3 as a BMI-associated gene, encoding an adaptor protein known to act downstream of BDNF and TrkB, which regulate appetite, food intake, and energy expenditure through unknown signaling pathways. The work presented here contributes to the biological foundation of obesity by providing a convincing downstream component of the BDNF-TrkB pathway, which could potentially be targeted for obesity treatment.
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spelling doaj-art-b24ecf182e4c47349175bacfde7801792025-08-20T02:10:14ZengNature PortfolioNature Communications2041-17232025-03-0116111610.1038/s41467-025-57753-2Missense variants in FRS3 affect body mass index in populations of diverse ancestriesAndrea B. Jonsdottir0Gardar Sveinbjornsson1Rosa B. Thorolfsdottir2Max Tamlander3Vinicius Tragante4Thorhildur Olafsdottir5Solvi Rognvaldsson6Asgeir Sigurdsson7Hannes P. Eggertsson8Hildur M. Aegisdottir9David O. Arnar10Karina Banasik11Doruk Beyter12Ragnar G. Bjarnason13Gyda Bjornsdottir14Søren Brunak15Mie Topholm Bruun16Joseph Dowsett17Eythor Einarsson18Gudmundur Einarsson19Christian Erikstrup20Run Fridriksdottir21Jonas Ghouse22Solveig Gretarsdottir23Gisli H. Halldorsson24Torben Hansen25Anna Helgadottir26Peter C. Holm27Erna V. Ivarsdottir28Kasper Karmark Iversen29Bitten Aagaard Jensen30Ingileif Jonsdottir31Stacey Knight32Kirk U. Knowlton33Snaedis Kristmundsdottir34Adalheidur E. Larusdottir35Olafur Th. Magnusson36Gisli Masson37Pall Melsted38Christina Mikkelsen39Kristjan H. S. Moore40Asmundur Oddsson41Pall I. Olason42Frosti Palsson43Ole Birger Pedersen44Michael Schwinn45Emil L. Sigurdsson46Aron Skaftason47Lilja Stefansdottir48Hreinn Stefansson49Thora Steingrimsdottir50Arni Sturluson51Unnur Styrkarsdottir52Erik Sørensen53Unnur D. Teitsdottir54Thorgeir E. Thorgeirsson55Gudmundur A. Thorisson56Unnur Thorsteinsdottir57Magnus O. Ulfarsson58Henrik Ullum59Arnor Vikingsson60G. Bragi Walters61DBDS Genomic ConsortiumLincoln D. Nadauld62Henning Bundgaard63Sisse Rye Ostrowski64Agnar Helgason65Bjarni V. Halldorsson66Gudmundur L. Norddahl67Samuli Ripatti68Daniel F. Gudbjartsson69Gudmar Thorleifsson70Valgerdur Steinthorsdottir71Hilma Holm72Patrick Sulem73Kari Stefansson74deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Institute for Molecular Medicine Finland, FIMM, HiLIFE, University of HelsinkideCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.The Novo Nordisk Foundation Center for Protein Research, Faculty of Health and Medical Sciences, University of CopenhagendeCODE genetics/Amgen Inc.Faculty of Medicine, School of Health Sciences, University of IcelanddeCODE genetics/Amgen Inc.The Novo Nordisk Foundation Center for Protein Research, Faculty of Health and Medical Sciences, University of CopenhagenDepartment of Clinical Immunology, Odense University HospitalDepartment of Clinical Immunology, Copenhagen University Hospital, RigshospitaletdeCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Department of Clinical Immunology, Aarhus University HospitaldeCODE genetics/Amgen Inc.Department of Cardiology, Copenhagen University Hospital, RigshospitaletdeCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.The Novo Nordisk Foundation Center for Basic Metabolic Research, Faculty of Health and Medical Sciences, University of CopenhagendeCODE genetics/Amgen Inc.The Novo Nordisk Foundation Center for Protein Research, Faculty of Health and Medical Sciences, University of CopenhagendeCODE genetics/Amgen Inc.Department of Cardiology, Copenhagen University Hospital, Herlev and Gentofte HospitalDepartment of Clinical Immunology, Aalborg University HospitaldeCODE genetics/Amgen Inc.Intermountain Medical Center, Intermountain Heart InstituteIntermountain Medical Center, Intermountain Heart InstitutedeCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Department of Clinical Immunology, Copenhagen University Hospital, RigshospitaletdeCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Department of Clinical Medicine, Faculty of Health and Medical Sciences, University of CopenhagenDepartment of Clinical Immunology, Copenhagen University Hospital, RigshospitaletFaculty of Medicine, School of Health Sciences, University of IcelanddeCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Faculty of Medicine, School of Health Sciences, University of IcelanddeCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Department of Clinical Immunology, Copenhagen University Hospital, RigshospitaletdeCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Statens Serum InstitutDepartment of Medicine, Landspitali - The National University Hospital of IcelanddeCODE genetics/Amgen Inc.Precision Genomics, Intermountain HealthcareDepartment of Cardiology, Copenhagen University Hospital, RigshospitaletDepartment of Clinical Immunology, Copenhagen University Hospital, RigshospitaletdeCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Institute for Molecular Medicine Finland, FIMM, HiLIFE, University of HelsinkideCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.deCODE genetics/Amgen Inc.Abstract Obesity is associated with adverse effects on health and quality of life. Improved understanding of its underlying pathophysiology is essential for developing counteractive measures. To search for sequence variants with large effects on BMI, we perform a multi-ancestry meta-analysis of 13 genome-wide association studies on BMI, including data derived from 1,534,555 individuals of European ancestry, 339,657 of Asian ancestry, and 130,968 of African ancestry. We identify an intergenic 262,760 base pair deletion at the MC4R locus that associates with 4.11 kg/m2 higher BMI per allele, likely through downregulation of MC4R. Moreover, a rare FRS3 missense variant, p.Glu115Lys, only found in individuals from Finland, associates with 1.09 kg/m2 lower BMI per allele. We also detect three other low-frequency FRS3 missense variants that associate with BMI with smaller effects and are enriched in different ancestries. We characterize FRS3 as a BMI-associated gene, encoding an adaptor protein known to act downstream of BDNF and TrkB, which regulate appetite, food intake, and energy expenditure through unknown signaling pathways. The work presented here contributes to the biological foundation of obesity by providing a convincing downstream component of the BDNF-TrkB pathway, which could potentially be targeted for obesity treatment.https://doi.org/10.1038/s41467-025-57753-2
spellingShingle Andrea B. Jonsdottir
Gardar Sveinbjornsson
Rosa B. Thorolfsdottir
Max Tamlander
Vinicius Tragante
Thorhildur Olafsdottir
Solvi Rognvaldsson
Asgeir Sigurdsson
Hannes P. Eggertsson
Hildur M. Aegisdottir
David O. Arnar
Karina Banasik
Doruk Beyter
Ragnar G. Bjarnason
Gyda Bjornsdottir
Søren Brunak
Mie Topholm Bruun
Joseph Dowsett
Eythor Einarsson
Gudmundur Einarsson
Christian Erikstrup
Run Fridriksdottir
Jonas Ghouse
Solveig Gretarsdottir
Gisli H. Halldorsson
Torben Hansen
Anna Helgadottir
Peter C. Holm
Erna V. Ivarsdottir
Kasper Karmark Iversen
Bitten Aagaard Jensen
Ingileif Jonsdottir
Stacey Knight
Kirk U. Knowlton
Snaedis Kristmundsdottir
Adalheidur E. Larusdottir
Olafur Th. Magnusson
Gisli Masson
Pall Melsted
Christina Mikkelsen
Kristjan H. S. Moore
Asmundur Oddsson
Pall I. Olason
Frosti Palsson
Ole Birger Pedersen
Michael Schwinn
Emil L. Sigurdsson
Aron Skaftason
Lilja Stefansdottir
Hreinn Stefansson
Thora Steingrimsdottir
Arni Sturluson
Unnur Styrkarsdottir
Erik Sørensen
Unnur D. Teitsdottir
Thorgeir E. Thorgeirsson
Gudmundur A. Thorisson
Unnur Thorsteinsdottir
Magnus O. Ulfarsson
Henrik Ullum
Arnor Vikingsson
G. Bragi Walters
DBDS Genomic Consortium
Lincoln D. Nadauld
Henning Bundgaard
Sisse Rye Ostrowski
Agnar Helgason
Bjarni V. Halldorsson
Gudmundur L. Norddahl
Samuli Ripatti
Daniel F. Gudbjartsson
Gudmar Thorleifsson
Valgerdur Steinthorsdottir
Hilma Holm
Patrick Sulem
Kari Stefansson
Missense variants in FRS3 affect body mass index in populations of diverse ancestries
Nature Communications
title Missense variants in FRS3 affect body mass index in populations of diverse ancestries
title_full Missense variants in FRS3 affect body mass index in populations of diverse ancestries
title_fullStr Missense variants in FRS3 affect body mass index in populations of diverse ancestries
title_full_unstemmed Missense variants in FRS3 affect body mass index in populations of diverse ancestries
title_short Missense variants in FRS3 affect body mass index in populations of diverse ancestries
title_sort missense variants in frs3 affect body mass index in populations of diverse ancestries
url https://doi.org/10.1038/s41467-025-57753-2
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