Nonalcoholic Steatohepatitis in a Patient with Ataxia-Telangiectasia

Ataxia-telangiectasia (A-T) is a rare disease characterized by neurodegenerative alterations, telangiectasia, primary immunodeficiency, extreme sensitivity to radiation, and susceptibility to neoplasms. A-T patients have inactivation of ataxia-telangiectasia-mutated (ATM) protein, which controls DNA...

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Bibliographic Details
Main Authors: Trinidad Caballero, Mercedes Caba-Molina, Javier Salmerón, Mercedes Gómez-Morales
Format: Article
Language:English
Published: Wiley 2014-01-01
Series:Case Reports in Hepatology
Online Access:http://dx.doi.org/10.1155/2014/761250
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