Infantile Systemic Hyalinosis Complicated with Right Atrial Thrombus and Pericardial Effusion in an Infant

Infantile systemic hyalinosis (ISH) is a rare multisystem fatal autosomal recessive disorder that involves widespread deposition of hyaline on connective tissues and certain internal organs. The major manifestations include painful articular contractures, hyperpigmentation, subcutaneous nodules, gin...

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Bibliographic Details
Main Authors: Sarar Mohamed, Wafa Ahmed, Nasir Al-Jurayyan, Eisa Faqeih, Abdulrahman Al-Nemri, Mohamed Al-Ghamdi
Format: Article
Language:English
Published: Elsevier 2017-02-01
Series:Pediatrics and Neonatology
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Online Access:http://www.sciencedirect.com/science/article/pii/S1875957214001624
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