Case Report: Contrasting outcomes and use of desmosine to monitor two patients treated with plasma cell-directed chemotherapy for gammopathy-driven pulmonary elastolysis in acquired cutis laxa

Case Report: Contrasting outcomes and use of desmosine to monitor two patients treated with plasma cell-directed chemotherapy for gammopathy-driven pulmonary elastolysis in acquired cutis laxa

Acquired cutis laxa (ACL) is a rare connective tissue disorder that is characterised by loose, pendulous skin and can be associated with systemic elastolysis and plasma cell dyscrasias (PCD). While myeloma therapy has been used for these patients, experience is limited, particularly when organ dysfu...

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Bibliographic Details
Main Authors: Lydia Lee, Emma Fosbury, Rakesh Popat, Kwee Yong, Ashutosh Wechalekar, Jeremy S. Brown, Jeffrey Huang, Sandy Mcbride, John R. Hurst
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-06-01
Series:Frontiers in Hematology
Subjects:
monoclonal gammopathies
acquired cutis laxa
desmosine
chemotherapy
elastolysis
Online Access:https://www.frontiersin.org/articles/10.3389/frhem.2025.1502322/full
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https://www.frontiersin.org/articles/10.3389/frhem.2025.1502322/full

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