Airway Management in a Patient with Wolf-Hirschhorn Syndrome
We present a case of a 3-month-old female with Wolf-Hirschhorn syndrome (WHS) undergoing general anesthesia for laparoscopic gastrostomy tube placement with a focus on airway management. WHS is a rare 4p microdeletion syndrome resulting in multiple congenital abnormalities, including craniofacial de...
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| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wiley
2016-01-01
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| Series: | Case Reports in Pediatrics |
| Online Access: | http://dx.doi.org/10.1155/2016/7070125 |
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| _version_ | 1832552439981539328 |
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| author | John F. Gamble Dinesh J. Kurian Andrea G. Udani Nathaniel H. Greene |
| author_facet | John F. Gamble Dinesh J. Kurian Andrea G. Udani Nathaniel H. Greene |
| author_sort | John F. Gamble |
| collection | DOAJ |
| description | We present a case of a 3-month-old female with Wolf-Hirschhorn syndrome (WHS) undergoing general anesthesia for laparoscopic gastrostomy tube placement with a focus on airway management. WHS is a rare 4p microdeletion syndrome resulting in multiple congenital abnormalities, including craniofacial deformities. Microcephaly, micrognathia, and glossoptosis are common features in WHS patients and risk factors for a pediatric airway that is potentially difficult to intubate. We discuss anesthesia strategies for airway preparation and management in a WHS patient requiring general anesthesia with endotracheal intubation. |
| format | Article |
| id | doaj-art-76448214ebb74503b13495af36d34fa3 |
| institution | Kabale University |
| issn | 2090-6803 2090-6811 |
| language | English |
| publishDate | 2016-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pediatrics |
| spelling | doaj-art-76448214ebb74503b13495af36d34fa32025-02-03T05:58:35ZengWileyCase Reports in Pediatrics2090-68032090-68112016-01-01201610.1155/2016/70701257070125Airway Management in a Patient with Wolf-Hirschhorn SyndromeJohn F. Gamble0Dinesh J. Kurian1Andrea G. Udani2Nathaniel H. Greene3Department of Anesthesiology, Duke University Medical Center, DUMC 3094, Durham, NC 27710, USADepartment of Anesthesiology, Duke University Medical Center, DUMC 3094, Durham, NC 27710, USADepartment of Anesthesiology, Duke University Medical Center, DUMC 3094, Durham, NC 27710, USADepartment of Anesthesiology, Duke University Medical Center, DUMC 3094, Durham, NC 27710, USAWe present a case of a 3-month-old female with Wolf-Hirschhorn syndrome (WHS) undergoing general anesthesia for laparoscopic gastrostomy tube placement with a focus on airway management. WHS is a rare 4p microdeletion syndrome resulting in multiple congenital abnormalities, including craniofacial deformities. Microcephaly, micrognathia, and glossoptosis are common features in WHS patients and risk factors for a pediatric airway that is potentially difficult to intubate. We discuss anesthesia strategies for airway preparation and management in a WHS patient requiring general anesthesia with endotracheal intubation.http://dx.doi.org/10.1155/2016/7070125 |
| spellingShingle | John F. Gamble Dinesh J. Kurian Andrea G. Udani Nathaniel H. Greene Airway Management in a Patient with Wolf-Hirschhorn Syndrome Case Reports in Pediatrics |
| title | Airway Management in a Patient with Wolf-Hirschhorn Syndrome |
| title_full | Airway Management in a Patient with Wolf-Hirschhorn Syndrome |
| title_fullStr | Airway Management in a Patient with Wolf-Hirschhorn Syndrome |
| title_full_unstemmed | Airway Management in a Patient with Wolf-Hirschhorn Syndrome |
| title_short | Airway Management in a Patient with Wolf-Hirschhorn Syndrome |
| title_sort | airway management in a patient with wolf hirschhorn syndrome |
| url | http://dx.doi.org/10.1155/2016/7070125 |
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