Interplay between iron metabolism, inflammation, and EPO-ERFE-hepcidin axis in RDEB-associated chronic anemia

Abstract: Recessive dystrophic epidermolysis bullosa (RDEB) is a genodermatosis characterized by severe cutaneous and mucosal fragility, and frequently complicated by multifactorial chronic anemia that responds poorly to conventional therapies. This cross-sectional study investigates the factors con...

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Main Authors: Lucía Quintana-Castanedo, Rocío Maseda, Isabel Pérez-Conde, Nora Butta, Elena Monzón-Manzano, Paula Acuña-Butta, María G. Crespo, Antonio Buño-Soto, Eva Jiménez, Jaris Valencia, María C. Arriba, Pilar Zuluaga, Raúl de Lucas, Marcela del Río, Ángeles Vicente, María J. Escámez, Rosa Sacedón
Format: Article
Language:English
Published: Elsevier 2025-05-01
Series:Blood Advances
Online Access:http://www.sciencedirect.com/science/article/pii/S2473952925001454
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