Pontocerebellar hypoplasia caused by the <i>TSEN54</i> mutation: clinical and electroencephalographic characteristics based on 3 cases

Pontocerebellar hypoplasia caused by the TSEN54 mutation is a severe hereditary disease with an autosomal recessive mode of inheritance, which is characterized by a combination of epileptic encephalopathy, motor disorders in the form of spasticity and hyperknesis, dysphagia and central respiratory f...

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Bibliographic Details
Main Authors: M. Yu. Bobylova, M. O. Abramov, K. Yu. Mukhin
Format: Article
Language:Russian
Published: ABV-press 2024-07-01
Series:Русский журнал детской неврологии
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Online Access:https://rjdn.abvpress.ru/jour/article/view/474
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