Successful treatment of post-pericardiotomy syndrome via C1 inhibitor replacement therapy in a hereditary angioedema patient with Marfan syndrome

Successful treatment of post-pericardiotomy syndrome via C1 inhibitor replacement therapy in a hereditary angioedema patient with Marfan syndrome

Background. Hereditary angioedema with C1 inhibitor deficiency (HAE-C1INH) is caused by dysfunctional C1-INH protein due to mutations in the SERPING1 gene encoding C1-INH. Marfan syndrome is a genetic connective tissue disease that affects the cardiovascular and ocular systems along with the...

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Bibliographic Details
Main Authors: Ezgi Topyıldız, Handan Duman Şenol, Figen Gülen, Esen Demir, Nihal Mete Gökmen
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2023-04-01
Series:The Turkish Journal of Pediatrics
Subjects:
C1 inhibitor replacement therapy
Marfan syndrome
hereditary angioedema
post-pericardiotomy syndrome
Online Access:https://turkjpediatr.org/article/view/40
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