Discordance between a deep learning model and clinical-grade variant pathogenicity classification in a rare disease cohort

Abstract Genetic testing is essential for diagnosing and managing clinical conditions, particularly rare Mendelian diseases. Although efforts to identify rare phenotype-associated variants have focused on protein-truncating variants, interpreting missense variants remains challenging. Deep learning...

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Bibliographic Details
Main Authors: Sek Won Kong, In-Hee Lee, Lauren V. Collen, Michael Field, Arjun K. Manrai, Scott B. Snapper, Kenneth D. Mandl
Format: Article
Language:English
Published: Nature Portfolio 2025-02-01
Series:npj Genomic Medicine
Online Access:https://doi.org/10.1038/s41525-025-00480-w
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