Extracellular domain shedding of NOTCH3 during endocytosis associated with heterogeneity between different CADASIL mutant activation mechanisms

Abstract Background Mutations in NOTCH3 cause CADASIL, a dominantly inherited condition, linked to recurrent stroke and vascular dementia and associated with accumulation of the ECD of NOTCH3. The latter has a toxic effect on VSMCs. Misregulated signalling may also play a role in disease progression...

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Bibliographic Details
Main Authors: Samira Hosseini-Alghaderi, Martin Baron
Format: Article
Language:English
Published: BMC 2025-08-01
Series:Cell Communication and Signaling
Online Access:https://doi.org/10.1186/s12964-025-02362-1
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