A case of relapsed gAChR-positive autoimmune autonomic ganglionopathy treated by plasma exchange and mycophenolate mofetil

A case of relapsed gAChR-positive autoimmune autonomic ganglionopathy treated by plasma exchange and mycophenolate mofetil

Autoimmune autonomic ganglionopathy (AAG) is a rare and acquired immune-mediated disease that leads to wide autonomic failure, mainly characterized by orthostatic hypotension, gastrointestinal dysfunction, anhidrosis and poorly reactive pupils. This disorder is usually associated with autoantibodies...

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Bibliographic Details
Main Authors:	Zhijie Lu, Xiaojie Cao, Mingyu Wang, Fang Peng, Lin Chen, Zegang Yin, Baiyang Zheng, Jin Fan, Mingjie Zhang
Format:	Article
Language:	English
Published:	Frontiers Media S.A. 2025-01-01
Series:	Frontiers in Neurology
Subjects:	autoimmune autonomic ganglionopathy ganglionic nicotinic acetylcholine receptor orthostatic hypotension gastrointestinal dysfunction case report
Online Access:	https://www.frontiersin.org/articles/10.3389/fneur.2024.1533840/full
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