The Transcriptional Activator Krüppel-like Factor-6 Is Required for CNS Myelination.

Growth factors of the gp130 family promote oligodendrocyte differentiation, and viability, and myelination, but their mechanisms of action are incompletely understood. Here, we show that these effects are coordinated, in part, by the transcriptional activator Krüppel-like factor-6 (Klf6). Klf6 is ra...

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Main Authors: Benjamin M Laitman, Linnéa Asp, John N Mariani, Jingya Zhang, Jia Liu, Setsu Sawai, Candice Chapouly, Sam Horng, Elisabeth G Kramer, Nesanet Mitiku, Hannah Loo, Natalie Burlant, Xiomara Pedre, Yuko Hara, German Nudelman, Elena Zaslavsky, Young-Min Lee, David A Braun, Q Richard Lu, Goutham Narla, Cedric S Raine, Scott L Friedman, Patrizia Casaccia, Gareth R John
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2016-05-01
Series:PLoS Biology
Online Access:https://journals.plos.org/plosbiology/article/file?id=10.1371/journal.pbio.1002467&type=printable
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author Benjamin M Laitman
Linnéa Asp
John N Mariani
Jingya Zhang
Jia Liu
Setsu Sawai
Candice Chapouly
Sam Horng
Elisabeth G Kramer
Nesanet Mitiku
Hannah Loo
Natalie Burlant
Xiomara Pedre
Yuko Hara
German Nudelman
Elena Zaslavsky
Young-Min Lee
David A Braun
Q Richard Lu
Goutham Narla
Cedric S Raine
Scott L Friedman
Patrizia Casaccia
Gareth R John
author_facet Benjamin M Laitman
Linnéa Asp
John N Mariani
Jingya Zhang
Jia Liu
Setsu Sawai
Candice Chapouly
Sam Horng
Elisabeth G Kramer
Nesanet Mitiku
Hannah Loo
Natalie Burlant
Xiomara Pedre
Yuko Hara
German Nudelman
Elena Zaslavsky
Young-Min Lee
David A Braun
Q Richard Lu
Goutham Narla
Cedric S Raine
Scott L Friedman
Patrizia Casaccia
Gareth R John
author_sort Benjamin M Laitman
collection DOAJ
description Growth factors of the gp130 family promote oligodendrocyte differentiation, and viability, and myelination, but their mechanisms of action are incompletely understood. Here, we show that these effects are coordinated, in part, by the transcriptional activator Krüppel-like factor-6 (Klf6). Klf6 is rapidly induced in oligodendrocyte progenitors (OLP) by gp130 factors, and promotes differentiation. Conversely, in mice with lineage-selective Klf6 inactivation, OLP undergo maturation arrest followed by apoptosis, and CNS myelination fails. Overlapping transcriptional and chromatin occupancy analyses place Klf6 at the nexus of a novel gp130-Klf-importin axis, which promotes differentiation and viability in part via control of nuclear trafficking. Klf6 acts as a gp130-sensitive transactivator of the nuclear import factor importin-α5 (Impα5), and interfering with this mechanism interrupts step-wise differentiation. Underscoring the significance of this axis in vivo, mice with conditional inactivation of gp130 signaling display defective Klf6 and Impα5 expression, OLP maturation arrest and apoptosis, and failure of CNS myelination.
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spelling doaj-art-2dfa39249e6546189fb8f3c3d17cf4452025-08-20T02:15:40ZengPublic Library of Science (PLoS)PLoS Biology1544-91731545-78852016-05-01145e100246710.1371/journal.pbio.1002467The Transcriptional Activator Krüppel-like Factor-6 Is Required for CNS Myelination.Benjamin M LaitmanLinnéa AspJohn N MarianiJingya ZhangJia LiuSetsu SawaiCandice ChapoulySam HorngElisabeth G KramerNesanet MitikuHannah LooNatalie BurlantXiomara PedreYuko HaraGerman NudelmanElena ZaslavskyYoung-Min LeeDavid A BraunQ Richard LuGoutham NarlaCedric S RaineScott L FriedmanPatrizia CasacciaGareth R JohnGrowth factors of the gp130 family promote oligodendrocyte differentiation, and viability, and myelination, but their mechanisms of action are incompletely understood. Here, we show that these effects are coordinated, in part, by the transcriptional activator Krüppel-like factor-6 (Klf6). Klf6 is rapidly induced in oligodendrocyte progenitors (OLP) by gp130 factors, and promotes differentiation. Conversely, in mice with lineage-selective Klf6 inactivation, OLP undergo maturation arrest followed by apoptosis, and CNS myelination fails. Overlapping transcriptional and chromatin occupancy analyses place Klf6 at the nexus of a novel gp130-Klf-importin axis, which promotes differentiation and viability in part via control of nuclear trafficking. Klf6 acts as a gp130-sensitive transactivator of the nuclear import factor importin-α5 (Impα5), and interfering with this mechanism interrupts step-wise differentiation. Underscoring the significance of this axis in vivo, mice with conditional inactivation of gp130 signaling display defective Klf6 and Impα5 expression, OLP maturation arrest and apoptosis, and failure of CNS myelination.https://journals.plos.org/plosbiology/article/file?id=10.1371/journal.pbio.1002467&type=printable
spellingShingle Benjamin M Laitman
Linnéa Asp
John N Mariani
Jingya Zhang
Jia Liu
Setsu Sawai
Candice Chapouly
Sam Horng
Elisabeth G Kramer
Nesanet Mitiku
Hannah Loo
Natalie Burlant
Xiomara Pedre
Yuko Hara
German Nudelman
Elena Zaslavsky
Young-Min Lee
David A Braun
Q Richard Lu
Goutham Narla
Cedric S Raine
Scott L Friedman
Patrizia Casaccia
Gareth R John
The Transcriptional Activator Krüppel-like Factor-6 Is Required for CNS Myelination.
PLoS Biology
title The Transcriptional Activator Krüppel-like Factor-6 Is Required for CNS Myelination.
title_full The Transcriptional Activator Krüppel-like Factor-6 Is Required for CNS Myelination.
title_fullStr The Transcriptional Activator Krüppel-like Factor-6 Is Required for CNS Myelination.
title_full_unstemmed The Transcriptional Activator Krüppel-like Factor-6 Is Required for CNS Myelination.
title_short The Transcriptional Activator Krüppel-like Factor-6 Is Required for CNS Myelination.
title_sort transcriptional activator kruppel like factor 6 is required for cns myelination
url https://journals.plos.org/plosbiology/article/file?id=10.1371/journal.pbio.1002467&type=printable
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