Oral trehalose improves histological and behavior symptoms of mucopolysaccharidosis type II in iduronate 2-sulfatase deficient mice

Abstract Mucopolysaccharidosis type II (MPS II) is caused by a deficiency in iduronate-2-sulfatase (Ids), an enzyme that catabolizes glycosaminoglycan (GAG). Ids insufficiency results in the accumulation of GAG in various organs, ultimately resulting in multisystemic disease. Trehalose, a non-reduci...

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Bibliographic Details
Main Authors: Hyesook Lee, Jung-Hwa Han, Roo Gam Jeong, Yun Jeong Kang, Byung Hyun Choi, Seo Rin Kim, Chong Kun Cheon, Jin Hur, Soo Yong Lee
Format: Article
Language:English
Published: Nature Portfolio 2025-02-01
Series:Scientific Reports
Online Access:https://doi.org/10.1038/s41598-025-88362-0
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