Overall mortality in combined pulmonary fibrosis and emphysema related to systemic sclerosis

Objectives This multicentre study aimed to investigate the overall mortality of combined pulmonary fibrosis and emphysema (CPFE) in systemic sclerosis (SSc) and to compare CPFE-SSc characteristics with those of other SSc subtypes (with interstitial lung disease—ILD, emphysema or neither).Methods Che...

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Main Authors: Carlo Alberto Scirè, Alarico Ariani, Mario Silva, Elena Bravi, Simone Parisi, Marta Saracco, Fabio De Gennaro, Cristian Caimmi, Francesco Girelli, Maria De Santis, Alessandro Volpe, Federica Lumetti, Vanessa Hax, Markus Bredemeier, Veronica Alfieri, Daniele Santilli, Flavio Cesare Bodini, Gianluca Lucchini, Flavio Mozzani, Valeria Seletti, Emanuele Bacchini, Eugenio Arrigoni, Dilia Giuggioli, Rafael Chakr, Luca Idolazzi, Giuseppina Bertorelli, Davide Imberti, Emanuele Michieletti, Giuseppe Paolazzi, Enrico Fusaro, Alfredo Antonio Chetta, Nicola Sverzellati
Format: Article
Language:English
Published: BMJ Publishing Group 2019-05-01
Series:RMD Open
Online Access:https://rmdopen.bmj.com/content/5/1/e000820.full
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