Gastrointestinal Involvement in Lipoid Proteinosis: A Ten-Year Follow-Up of a Brazilian Female Patient

Lipoid proteinosis is a rare autosomal recessive disease characterized by the deposition of hyaline material in the skin and internal organs. The main clinical features are hoarseness and typical skin lesions. In this report we describe the endoscopic and radiologic findings in a Brazilian female pa...

Full description

Saved in:
Bibliographic Details
Main Authors: Juliana Custódio Lima, Cristiane Kibune Nagasako, Ciro Garcia Montes, Irene Harumi Kamata Barcelos, Rita Barbosa de Carvalho, Maria Aparecida Mesquita
Format: Article
Language:English
Published: Wiley 2014-01-01
Series:Case Reports in Medicine
Online Access:http://dx.doi.org/10.1155/2014/952038
Tags: Add Tag
No Tags, Be the first to tag this record!