LRG1 Alters Pericyte Phenotype and Compromises Vascular Maturation

Upregulation of leucine-rich alpha-2-glycoprotein-1 (LRG1) contributes to aberrant neovascularization in many different diseases. In contrast, LRG1 is not involved in developmental angiogenesis. Here, we investigated the vasculopathic properties of LRG1 by examining its effect on developing retinal...

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Main Authors: Alexandra E. Hoeh, Jui-Hsien Chang, Ronja S. Mueller, Mark Basche, Alessandro Fantin, Anastasios Sepetis, Giulia De Rossi, Athina Dritsoula, Robin R. Ali, Patric Turowski, Stephen E. Moss, John Greenwood
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Language:English
Published: MDPI AG 2025-04-01
Series:Cells
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Online Access:https://www.mdpi.com/2073-4409/14/8/593
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author Alexandra E. Hoeh
Jui-Hsien Chang
Ronja S. Mueller
Mark Basche
Alessandro Fantin
Anastasios Sepetis
Giulia De Rossi
Athina Dritsoula
Robin R. Ali
Patric Turowski
Stephen E. Moss
John Greenwood
author_facet Alexandra E. Hoeh
Jui-Hsien Chang
Ronja S. Mueller
Mark Basche
Alessandro Fantin
Anastasios Sepetis
Giulia De Rossi
Athina Dritsoula
Robin R. Ali
Patric Turowski
Stephen E. Moss
John Greenwood
author_sort Alexandra E. Hoeh
collection DOAJ
description Upregulation of leucine-rich alpha-2-glycoprotein-1 (LRG1) contributes to aberrant neovascularization in many different diseases. In contrast, LRG1 is not involved in developmental angiogenesis. Here, we investigated the vasculopathic properties of LRG1 by examining its effect on developing retinal blood vessels. By injecting recombinant protein or an expression vector into the mouse retina during vascular development, we showed that exogenous LRG1 reduces pericyte coverage and NG2 expression. It leads to diminished collagen IV sheathing, fewer adhesion and gap junctions, and reduced vessel calibre and vascular density. Moreover, in mouse retinae containing exogenous LRG1, the developing blood–retinal barrier remains more permeable with significantly higher numbers of transcytotic vesicles present in microvascular endothelial cells. These results reveal that exogeneous LRG1 is sufficient to interfere with the maturation of developing retinal vessels and drive vessel development towards a dysfunctional phenotype. These observations deliver further evidence that LRG1 is an angiopathic factor and highlight the therapeutic potential of blocking LRG1 in diseases characterized by pathogenic angiogenesis or vascular remodelling.
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spelling doaj-art-02eae5e725de4ded879e1bd0237cba782025-08-20T02:24:42ZengMDPI AGCells2073-44092025-04-0114859310.3390/cells14080593LRG1 Alters Pericyte Phenotype and Compromises Vascular MaturationAlexandra E. Hoeh0Jui-Hsien Chang1Ronja S. Mueller2Mark Basche3Alessandro Fantin4Anastasios Sepetis5Giulia De Rossi6Athina Dritsoula7Robin R. Ali8Patric Turowski9Stephen E. Moss10John Greenwood11Institute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKDepartment of Biosciences, University of Milan, 20133 Milan, ItalyInstitute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKInstitute of Ophthalmology, University College London, London EC1V 9EL, UKUpregulation of leucine-rich alpha-2-glycoprotein-1 (LRG1) contributes to aberrant neovascularization in many different diseases. In contrast, LRG1 is not involved in developmental angiogenesis. Here, we investigated the vasculopathic properties of LRG1 by examining its effect on developing retinal blood vessels. By injecting recombinant protein or an expression vector into the mouse retina during vascular development, we showed that exogenous LRG1 reduces pericyte coverage and NG2 expression. It leads to diminished collagen IV sheathing, fewer adhesion and gap junctions, and reduced vessel calibre and vascular density. Moreover, in mouse retinae containing exogenous LRG1, the developing blood–retinal barrier remains more permeable with significantly higher numbers of transcytotic vesicles present in microvascular endothelial cells. These results reveal that exogeneous LRG1 is sufficient to interfere with the maturation of developing retinal vessels and drive vessel development towards a dysfunctional phenotype. These observations deliver further evidence that LRG1 is an angiopathic factor and highlight the therapeutic potential of blocking LRG1 in diseases characterized by pathogenic angiogenesis or vascular remodelling.https://www.mdpi.com/2073-4409/14/8/593leucine-rich alpha-2-glycoprotein-1 (LRG1)pericyteblood–retinal barrierangiogenesisblood vessel maturation
spellingShingle Alexandra E. Hoeh
Jui-Hsien Chang
Ronja S. Mueller
Mark Basche
Alessandro Fantin
Anastasios Sepetis
Giulia De Rossi
Athina Dritsoula
Robin R. Ali
Patric Turowski
Stephen E. Moss
John Greenwood
LRG1 Alters Pericyte Phenotype and Compromises Vascular Maturation
Cells
leucine-rich alpha-2-glycoprotein-1 (LRG1)
pericyte
blood–retinal barrier
angiogenesis
blood vessel maturation
title LRG1 Alters Pericyte Phenotype and Compromises Vascular Maturation
title_full LRG1 Alters Pericyte Phenotype and Compromises Vascular Maturation
title_fullStr LRG1 Alters Pericyte Phenotype and Compromises Vascular Maturation
title_full_unstemmed LRG1 Alters Pericyte Phenotype and Compromises Vascular Maturation
title_short LRG1 Alters Pericyte Phenotype and Compromises Vascular Maturation
title_sort lrg1 alters pericyte phenotype and compromises vascular maturation
topic leucine-rich alpha-2-glycoprotein-1 (LRG1)
pericyte
blood–retinal barrier
angiogenesis
blood vessel maturation
url https://www.mdpi.com/2073-4409/14/8/593
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