Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery
Freeman-Sheldon syndrome (FSS) or “whistling face” syndrome is a rare congenital disorder complicated by characteristic facial deformities and muscular contractures. We report on a 64-year-old male patient presenting for surgical replacement of his aortic valve and review the available literature on...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Anesthesiology |
| Online Access: | http://dx.doi.org/10.1155/2018/7862327 |
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| author | S. Viehmeyer P. Gabriel K. Bauer S. Bauer R. Sodian J. N. Hilberath |
| author_facet | S. Viehmeyer P. Gabriel K. Bauer S. Bauer R. Sodian J. N. Hilberath |
| author_sort | S. Viehmeyer |
| collection | DOAJ |
| description | Freeman-Sheldon syndrome (FSS) or “whistling face” syndrome is a rare congenital disorder complicated by characteristic facial deformities and muscular contractures. We report on a 64-year-old male patient presenting for surgical replacement of his aortic valve and review the available literature on anesthetic considerations and perioperative management principles. FSS frequently poses a significant challenge to airway management and gaining vascular access. Moreover, these patients are reportedly at risk for developing malignant hyperthermia (MH) or neuroleptic malignant syndrome. |
| format | Article |
| id | doaj-art-02a9b595c61f40069b56ba59d6cd32ad |
| institution | Kabale University |
| issn | 2090-6382 2090-6390 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Anesthesiology |
| spelling | doaj-art-02a9b595c61f40069b56ba59d6cd32ad2025-02-03T07:25:20ZengWileyCase Reports in Anesthesiology2090-63822090-63902018-01-01201810.1155/2018/78623277862327Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart SurgeryS. Viehmeyer0P. Gabriel1K. Bauer2S. Bauer3R. Sodian4J. N. Hilberath5Department of Anesthesiology and Critical Care Medicine, MediClin Heart Institute Lahr/Baden, Lahr, GermanyDepartment of Anesthesiology and Critical Care Medicine, MediClin Heart Institute Lahr/Baden, Lahr, GermanyDepartment of Cardiac Surgery, MediClin Heart Institute Lahr/Baden, Lahr, GermanyDepartment of Cardiac Surgery, MediClin Heart Institute Lahr/Baden, Lahr, GermanyDepartment of Cardiac Surgery, MediClin Heart Institute Lahr/Baden, Lahr, GermanyDepartment of Anesthesiology and Critical Care Medicine, MediClin Heart Institute Lahr/Baden, Lahr, GermanyFreeman-Sheldon syndrome (FSS) or “whistling face” syndrome is a rare congenital disorder complicated by characteristic facial deformities and muscular contractures. We report on a 64-year-old male patient presenting for surgical replacement of his aortic valve and review the available literature on anesthetic considerations and perioperative management principles. FSS frequently poses a significant challenge to airway management and gaining vascular access. Moreover, these patients are reportedly at risk for developing malignant hyperthermia (MH) or neuroleptic malignant syndrome.http://dx.doi.org/10.1155/2018/7862327 |
| spellingShingle | S. Viehmeyer P. Gabriel K. Bauer S. Bauer R. Sodian J. N. Hilberath Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery Case Reports in Anesthesiology |
| title | Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery |
| title_full | Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery |
| title_fullStr | Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery |
| title_full_unstemmed | Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery |
| title_short | Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery |
| title_sort | anesthetic considerations for an adult patient with freeman sheldon syndrome undergoing open heart surgery |
| url | http://dx.doi.org/10.1155/2018/7862327 |
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