Inflammation in Cystic Fibrosis

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Lobectomy in Patients with Cystic Fibrosis by Shahid I Sheikh, Karen McCoy, Nancy A Ryan-Wenger, Alpa Patel, Stephen Kirkby

“…BACKGROUND: Some patients with cystic fibrosis (CF) develop severe but localized lung disease or recurrent hemoptysis/pneumothorax refractory to conventional medical therapies.…”
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Pseudomonas cepacia in cystic fibrosis by Ronald Gold

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Imaging the Abdominal Manifestations of Cystic Fibrosis by C. D. Gillespie, M. K. O’Reilly, G. N. Allen, S. McDermott, V. O. Chan, C. A. Ridge

“…Cystic fibrosis (CF) is a multisystem disease with a range of abdominal manifestations including those involving the liver, pancreas, and kidneys. …”
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MicroRNA Dysregulation in Cystic Fibrosis by Paul J. McKiernan, Catherine M. Greene

“…The cystic fibrosis lung is a complex milieu comprising multiple factors that coordinate its physiology. …”
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Cystic Fibrosis: Bench to Bedside 2003 by Bruce K Rubin

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Liver Transplantation for Cirrhosis in Cystic Fibrosis by T Lamireau, S Martin, M Lallier, JE Marcotte, F Alvarez

“…BACKGROUND: Liver disease is the third most common cause of death in children with cystic fibrosis (CF). Liver transplantation is an effective treatment in children with hepatic failure.…”
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Epidemiology of Pseudomonas cepacia in Cystic Fibrosis by Statement from the Medical/Scientific Advisory Committee Canadian Cystic Fibrosis Foundation

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A Roadmap to the Brittle Bones of Cystic Fibrosis by Ashwini P. Gore, Soon Ho Kwon, Antine E. Stenbit

“…Cystic fibrosis (CF) is an autosomal recessive disorder which despite advances in medical care continues to be a life-limiting and often fatal disease. …”
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Characterization of Patients with Cystic Fibrosis in Multidisciplinary Consultation by Caridad Llull Tombo, Mercedes Fonseca Hernández, Ileana García Rodríguez, Juan Carlos Yanes Macías, Daymí Tió González, Yoandra León Rayas

“…<strong><br />Objective:</strong> to characterize patients with cystic fibrosis in the province of Cienfuegos.<strong><br /> Methods:</strong> an observational, descriptive and cross-sectional study was carried out at the Paquito González Cueto de Cienfuegos University Pediatric Hospital in the cystic fibrosis consultation, from January 1 to December 31, 2018. …”
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Paradoxical Embolization in an Adult Cystic Fibrosis Patient by Nabil M Al Lawati, Pearce Wilcox

“…Cystic fibrosis patients with an implantable venous access device (IVAD) and a patent foramen ovale (PFO) are at an increased risk of developing paradoxical embolism. …”
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New Developments in Cystic Fibrosis Airway Inflammation by Nades Palaniyar, Marcus A. Mall, Christian Taube, Stefan Worgall, Hartmut Grasemann

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Progressive Scoliosis in a Child with Cystic Fibrosis by Lauren M. Castner, Samya Z. Nasr, Manuel Arteta

“…We discuss an adolescent female with cystic fibrosis, asthma, and scoliosis who had a rapid decline in her pulmonary function despite typical treatment for a cystic fibrosis exacerbation. …”
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Pancreatic Cystosis in Two Adolescents with Cystic Fibrosis by Elpis Hatziagorou, Asterios Kampouras, Maria Sidiropoulou, Andreas Markou, Athanasia Anastasiou, John Tsanakas

“…We present pancreatic cystosis in two adolescents with cystic fibrosis, a 13-year-old girl and an 18-year-old boy. …”
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Pulmonary Nocardiosis in an Immunocompetent Patient with Cystic Fibrosis by Lucy Schoen, Jonathan D. Santoro, Carlos Milla, Sumit Bhargava

“…Nocardia spp. are bacteria of low virulence that cause infection classically in immunocompromised hosts with the lungs as the primary site of infection in the majority of cases. Patients with cystic fibrosis have pulmonary disease characterized by frequent and progressive bacterial infections. …”
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Psychometric validation of the Cystic Fibrosis Impact Questionnaire (CF-IQ): A patient-reported outcome assessing impacts of cystic fibrosis. by Daniel Serrano, Alyssa Uzumcu, Maya Gerstein, Nicolai D Ayasse, Ella Engstrom, Frederick B Barnes, Charles Iaconangelo, Teja Thorat, Lisa J McGarry, Isabelle Sermet-Gaudelus

“…The Cystic Fibrosis (CF) Impact Questionnaire (CF-IQ) was qualitatively developed to assess the impact of CF in the context of treatment advancements and increased longevity. …”
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Aquagenic Wrinkling of the Palms in a Patient with Cystic Fibrosis by Inês Aparício Martins, Miguel Santos-Coelho, Cândida Fernandes

Subjects: “…Cystic Fibrosis…”
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Adrenal Insufficiency in Cystic Fibrosis: A Rare Phenomenon? by Sébastien Préville-Ratelle, Adèle Coriati, Aurélie Ménard, Isabelle Bourdeau, François Tremblay, Yves Berthiaume

“…The prevalence of adrenal insufficiency (AI) in cystic fibrosis (CF) is unknown. The frequent use of glucocorticoids (inhaled or systemic) may induce the long-term suppression of the hypothalamic-pituitary-adrenal axis. …”
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Catamenial Hemoptysis and Pneumothoraces in a Patient with Cystic Fibrosis by Chris M Parker, Robert Nolan, M Diane Lougheed

“…A 32-year-old woman with cystic fibrosis, who over a period of several months had experienced recurrent catamenial hemoptysis and pneumothoraces, including an episode of life-threatening hemoptysis that coincided with menstruation, is presented. …”
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Cepacia Syndrome in a Non-Cystic Fibrosis Patient by Naomi Hauser, Jose Orsini

“…The potential for this pathogen to infect non-cystic fibrosis patients is limited and its epidemiology is poorly understood. …”
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