Proteomics profiling of inflammatory responses to elexacaftor/tezacaftor/ivacaftor in cystic fibrosis by Hazel Ozuna, Hazel Ozuna, Dinesh Bojja, Santiago Partida-Sanchez, Luanne Hall-Stoodley, Amal Amer, Rodney D. Britt, Rodney D. Britt, Shahid Sheikh, David A. Frank, Weiyuan Wang, Bum-Yong Kang, Bum-Yong Kang, Irina Miralda, Irina Miralda, Samantha L. Durfey, Samantha L. Durfey, Benjamin T. Kopp, Benjamin T. Kopp

Subjects: “…cystic fibrosis…”
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Patient Perspectives on the Use of Digital Technology to Help Manage Cystic Fibrosis by Alexandre H. Watanabe, Connor Willis, Russell Ragsdale, Joseph Biskupiak, Karlene Moore, Diana Brixner, David Young

“…Digital health technologies (DHTs) have shown potential to improve health outcomes through improved medication adherence in different disease states. Cystic fibrosis (CF) requires care coordination across pharmacies, patients, and providers. …”
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Anesthetic Management and Considerations for Cesarean Delivery in a Patient With Cystic Fibrosis by Richard Pham, Chris Mehdizadeh, Christopher Baker, Leonard J. Soloniuk, Ioana Pasca, Ashish Sinha

“…Recent advancements in therapeutics and risk reduction in the management of cystic fibrosis have increased the life expectancy of cystic fibrosis patients to the fifth decade of life. …”
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Mixed Comparative Evaluation of a Training Program Dedicated to Cystic Fibrosis Reference Centers: Protocol for the Pilot Implementation of Shared Decision-Making in the Treatment of Diabetes in Adult Patients With Cystic Fibrosis by Nora Moumjid, Constance Gotte, Sophie Hommey, Stéphanie Poupon Bourdy, Julie Haesebaert, Isabelle Durieu, Quitterie Reynaud

“…Two treatment options are possible: start insulin as soon as cystic fibrosis diagnosis is made with the additional constraints of cystic fibrosis or wait while monitoring the patient’s clinical condition and start insulin when diabetes symptoms develop and therefore later. …”
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Distribution and Characteristics of Bacteria Isolated from Cystic Fibrosis Patients with Pulmonary Exacerbation by Soroor Erfanimanesh, Mohammad Emaneini, Mohammad Reza Modaresi, Mohammad Mehdi Feizabadi, Shahnaz Halimi, Reza Beigverdi, Vajiheh Sadat Nikbin, Fereshteh Jabalameli

“…Background. Cystic fibrosis (CF) is an inherited recessive disorder characterized by recurrent and persistent pulmonary infections, resulting in lung function deterioration and early mortality. …”
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New era, new GOALs: cardiovascular screening and lipid management in cystic fibrosis by Katherine A. Despotes, Agathe S. Ceppe, Jennifer L. Goralski, Scott H. Donaldson

“…Background: Cardiovascular disease (CVD) risks are increasing in people with cystic fibrosis (pwCF). While cholesterol levels were historically low in pwCF, higher levels after initiating highly effective modulator therapy (HEMT) have been reported. …”
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Higher Mobility Scores in Patients with Cystic Fibrosis Are Associated with Better Lung Function by Aneesha Thobani, Jessica A. Alvarez, Shaina Blair, Kaila Jackson, Eric R. Gottlieb, Seth Walker, Vin Tangpricha

“…The purpose of this study was to determine whether mobility and physical activity were associated with lung function in adults with cystic fibrosis (CF). Design. This was a prospective cohort observational study in an urban, academic, specialized care center. …”
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Acute Muscle Trauma due to Overexercise in an Otherwise Healthy Patient with Cystic Fibrosis by Henning Neubauer, Clemens Wirth, Katharina Ruf, Helge Hebestreit, Meinrad Beer

“…Cystic fibrosis (CF) is one of the most common inherited diseases and is caused by mutations in the CFTR gene. …”
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Understanding biofilm--phage interactions in cystic fibrosis patients using mathematical frameworks by Emerenini Blessing O., Hartung Doris, Reyes Grimaldo Ricardo N. G., Canner Claire, Williams Maya, Agyingi Ephraim, Osgood Robert

“…Certain lung diseases such as cystic fibrosis can cause the formation of biofilms in the lungs and can be fatal. …”
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Drug Reaction with Eosinophilia and Systemic Symptoms Syndrome in a Child with Cystic Fibrosis by Ahmed Abushahin, Haneen Toma, Sara G. Hamad, Mutasim Abu-Hasan

“…A 2.5-year-old boy with known diagnosis of cystic fibrosis, bilateral bronchiectasis, pancreatic insufficiency, and chronic airway colonization with Pseudomonas aeruginosa was admitted to our hospital with acute pulmonary exacerbation of CF lung disease. …”
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Psychosocial and mental health in cystic fibrosis in the modern era of care: time to evolve by Beth Smith, Tonia A Douglas, Alexandra L Quittner, Anna M Georgiopoulos, Maggie Harrigan

“…Cystic fibrosis (CF) treatment has revolutionised care over the past three decades with major advances in survival. …”
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Serum Hepcidin Level as a Marker of Iron Status in Children with Cystic Fibrosis by Monika Kałużna-Czyż, Urszula Grzybowska-Chlebowczyk, Halina Woś, Sabina Więcek

“…Material and Methods. 46 children with cystic fibrosis and 31 healthy controls were enrolled. …”
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Impact of elexacaftor-tezacaftor-ivacaftor in lung transplantation for cystic fibrosis in the United States by Tahuanty A. Pena, MD, MS, Brittany Wright, PharmD, Kalpaj R. Parekh, MBBS, Julia Kleney-Tait, MD, PhD

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Metastatic Bladder Cancer Presenting with Persistent Hematuria in Young Man with Cystic Fibrosis by Premal Patel, Harvey R. Rabin, Michael M. Vickers, Michael D. Parkins

“…We report a case of metastatic bladder cancer developing in a young man with cystic fibrosis (CF) that was initially diagnosed as ureterolithiasis and managed as renal colic. …”
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Scoping review: relationship between glucose tolerance and pulmonary decline in cystic fibrosis by Raina Tomoda, Deborah Jane Holmes-Walker

“… Cystic fibrosis-related diabetes (CFRD) causes deterioration of cystic fibrosis (CF) lung disease, thereby increasing mortality. …”
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Additive Effect of Dornase Alfa and Nacystelyn on Transportability and Viscoelasticity of Cystic Fibrosis Sputum by Feng Sun, Shusheng Tai, Thomas Lim, Ulrich Baumann, Malcolm King

“…OBJECTIVE: To investigate the effect of dornase alfa (DA), Nacystelyn (NAL) and their combination on mucociliary transportability and mucus viscoelasticity of cystic fibrosis (CF) sputum, and to assess whether the combination possesses an additive effect.…”
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Anti-inflammatory and immunomodulating effects of clarithromycin in patients with cystic fibrosis lung disease by Alexander L. Pukhalsky, Galina V. Shmarina, Nikolai I. Kapranov, Svetlana N. Kokarovtseva, Daria Pukhalskaya, Natalia J. Kashirskaja

“…BACKGROUND and aim: Macrolide antibiotics are widely used in the treatment of suppurative lung diseases including cystic fibrosis (CF), the most common inherited fatal disease in the Caucasian population. …”
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Efficacy of melatonin treatment in a cystic fibrosis mouse model of airway infection by Kristen R. Schaefer, Sara Rogers, Zachary Faber, Thomas J. Kelley

“…Abstract Approaches to mitigate the severity of infections and of immune responses are still needed for the treatment of cystic fibrosis (CF) even with the success of highly effective modulator therapies. …”
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Improvement of nutrient absorption may enhance systemic oxidative stress in cystic fibrosis patients by Galina V. Shmarina, Alexander L. Pukhalsky, Svetlana N. Kokarovtseva, Daria A. Pukhalskaya, Elena A. Kalashnikova, Nikolaï I. Kapranov, Natalia J. Kashirskaja

“…Background: The life expectancy of patients with cystic fibrosis (CF) is largely dependent on the pulmonary disease severity and progress. …”
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Spirometry-Related Pain and Distress in Adolescents and Young Adults with Cystic Fibrosis: The Role of Acceptance by Annabelle Casier, Liesbet Goubert, Tine Vervoort, Marleen Theunis, Danielle Huse, Frans De Baets, Dirk Matthys, Geert Crombez

“…OBJECTIVE: To investigate the occurrence of spirometry-related pain and distress in adolescents and young adults with cystic fibrosis (CF), and to investigate the role of acceptance of illness in spirometry-related pain and distress.…”
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