Protease-activated receptor 1 in the pathogenesis of cystic fibrosis by Sarath Ranganathan, Philip Sutton, Sophie Day, Poshmaal Dhar, Kristy Azzopardi, Muhammad A Saeed, Sohinee Sarkar, Jia-Xi Han

“…Background The most common cause of death in those with cystic fibrosis (CF) is respiratory failure due to bronchiectasis resulting from repeated cycles of respiratory infection and inflammation. …”
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The Role of Serine Proteases and Antiproteases in the Cystic Fibrosis Lung by Matthew S. Twigg, Simon Brockbank, Philip Lowry, S. Peter FitzGerald, Clifford Taggart, Sinéad Weldon

“…Cystic fibrosis (CF) lung disease is an inherited condition with an incidence rate of approximately 1 in 2500 new born babies. …”
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The Involvement of Glycosaminoglycans in Airway Disease Associated with Cystic Fibrosis by Emer P. Reeves, David A. Bergin, Michelle A. Murray, Noel G. McElvaney

“…Individuals with cystic fibrosis (CF) present with severe airway destruction and extensive bronchiectasis. …”
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Update of Faecal Markers of Inflammation in Children with Cystic Fibrosis by Jung M. Lee, Steven T. Leach, Tamarah Katz, Andrew S. Day, Adam Jaffe, Chee Y. Ooi

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Hepatic Abscess due to Burkholderia (Pseudomonas) cepacia in Cystic Fibrosis by Kristin L Fraser, Robert H Hyland, D Elizabeth Tullis

“…Two patients with cystic fibrosis are described who developed hepatic abscesses clue to B cepacia. …”
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Piperacillin-Induced Immune Hemolytic Anemia in an Adult with Cystic Fibrosis by Mahesh Bandara, David B. Seder, George Garratty, Regina M. Leger, Jonathan B. Zuckerman

“…We report a case of drug-induced immune hemolytic anemia (DIIHA) in an adult female with cystic fibrosis (CF), complicating routine treatment of a pulmonary exacerbation with intravenous piperacillin-tazobactam. …”
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Exercise Training in Children and Adolescents with Cystic Fibrosis: Theory into Practice by Craig A. Williams, Christian Benden, Daniel Stevens, Thomas Radtke

“…Physical activity and exercise training play an important role in the clinical management of patients with cystic fibrosis (CF). Exercise training is more common and recognized as an essential part of rehabilitation programmes and overall CF care. …”
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A new era of cystic fibrosis therapy with CFTR modulators by Laura Gomes Boabaid de Barros, Laura Menestrino Prestes, Maria Fernanda Gonçalves Meirelles Fernandes, Luiz Vicente Ribeiro Ferreira da Silva-Filho, Leonardo Araújo Pinto

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Quantitative ultrasound rating of liver fibrosis in children with cystic fibrosis by G. M. Dvoryakovskaya, O. I. Simonova, S. A. Ivleva, I. V. Dvoryakovsky, A. N. Surkov, M. O. Gorbunova, I. E. Smirnov

Subjects: “…cystic fibrosis in children…”
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Treatment of Pseudomonas and Staphylococcus Bronchopulmonary Infection in Patients with Cystic Fibrosis by Rashmi Ranjan Das, Sushil Kumar Kabra, Meenu Singh

“…The optimal antibiotic regimen is unclear in management of pulmonary infections due to pseudomonas and staphylococcus in cystic fibrosis (CF). We systematically searched all the published literature that has considered the evidence for antimicrobial therapies in CF till June 2013. …”
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Celiac Disease in Patients with Cystic Fibrosis-Related Bone Disease by Melissa S. Putman, Alexandra Haagensen, Isabel Neuringer, Leonard Sicilian

“…Both cystic fibrosis (CF) and celiac disease can cause low bone mineral density (BMD) and fractures. …”
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Cystic Fibrosis and Reproductive Outcomes: The Latest Insights into Fertility and Pregnancy by Weronika Małagocka, Karol Zagórski, Mateusz Kozik, Nina Skalska-Dziobek, Karolina Chybowska, Maria Naruszewicz, Przemysław Cetnarowski

Subjects: “…Cystic fibrosis…”
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An Unusual Case of Cystic Fibrosis Associated Pneumocystis jiroveci Pneumonia in an Infant by Ravinder Kaur, Priyanka Katariya, Megh Singh Dhakad, Bhanu Mehra, Urmila Jhamb, A. P. Dubey

“…Sweat chloride test for diagnosis of cystic fibrosis was positive. Bronchoalveolar lavage (BAL) fluid was collected and Pseudomonas aeruginosa was isolated on culture. …”
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When Women with Cystic Fibrosis Become Mothers: Psychosocial Impact and Adjustments by Sophie L. Cammidge, Alistair J. A. Duff, Gary J. Latchford, Christine Etherington

“…Advances in the treatment and life expectancy of cystic fibrosis (CF) patients mean that motherhood is now a realistic option for many women with CF. …”
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Suppurative Mediastinitis Secondary to Burkholderia Cepacia in a Patient with Cystic Fibrosis by Ronald B George, Yannick Cartier, Alan G Casson, Paul Hernandez

“…Burkholderia cepacia is an important opportunistic pathogen among patients with cystic fibrosis (CF); it is associated with deterioration of lung function, poor outcome following lung transplantation and increased mortality. …”
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Cystic Fibrosis Atypical Forms Presentation: Edema, Anemia and Skin Lesions by Chabelys de la Caridad Rodríguez Membrides, Carlos Enrique Cruz Carrazana, Milda Díaz Martínez

“…This case is presented for describing the clinical and laboratory characteristics of a patient with atypical presentation of cystic fibrosis. Skin alterations as a presenting sign of cystic fibrosis are rare and only fewer than 30 cases have been reported in the medical literature.…”
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Free DNA in Cystic Fibrosis Airway Fluids Correlates with Airflow Obstruction by Veronica Marcos, Zhe Zhou-Suckow, Ali Önder Yildirim, Alexander Bohla, Andreas Hector, Ljubomir Vitkov, Wolf Dietrich Krautgartner, Walter Stoiber, Matthias Griese, Oliver Eickelberg, Marcus A. Mall, Dominik Hartl

“…Chronic obstructive lung disease determines morbidity and mortality of patients with cystic fibrosis (CF). CF airways are characterized by a nonresolving neutrophilic inflammation. …”
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Pseudomonas Aeruginosa and Cystic Fibrosis: Antibiotic Therapy and the Science behind the Magic by Noni E MacDonald

“…Respiratory failure secondary to chronic bronchiectasis is the cause of death in more than 90% of patients with cystic fibrosis (CF). The predominant microbes involved in CF lung disease are unusual: Pseudomonas aeruginosa, Staphylococcus aureus and Burkolderia cepacia. …”
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Intracerebral Abscess: A Complication of Severe Cystic Fibrosis Lung Disease by Mark E Fenton, Donald W Cockcroft, John A Gjevre

“…Intracerebral abscess in cystic fibrosis and the potential role of pneumonectomy in the present patient are discussed.…”
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Outcomes of segmentectomy versus lobectomy in adults with non-cystic fibrosis bronchiectasis by José de Sá Moraes Neto, Isabele Alves Chirichela, Alessandro Wasum Mariani, Ricardo Mingarini Terra, Paulo Manuel Pêgo Fernandes

“…We sought to investigate the efficacy of sublobar resection (segmentectomy) and compare it with that of lobar resection (lobectomy) in patients with non-cystic fibrosis bronchiectasis. Methods: Patients undergoing lobectomy or segmentectomy between 2019 and 2023 were included in the study. …”
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