Defective Cystic Fibrosis Transmembrane Conductance Regulator Accelerates Skeletal Muscle Aging by Impairing Autophagy/Myogenesis by Ziyi Chen, Jiankun Xu, Peijie Hu, Wanting Du, Junjiang Chen, Xiaotian Zhang, Wei Zhou, Jiayang Gao, Yuantao Zhang, Bingyang Dai, Guangshuai Nie, Jun Hu, Liangbin Zhou, Shunxiang Xu, Hisao Chang Chan, Wing‐hoi Cheung, Ye Chun Ruan, Ling Qin

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Evaluation of the Effectiveness of Using the CFTR Modulator Ivacaftor/Lumacaftor in Children with Cystic Fibrosis in the Sverdlovsk Region (Prospective Cohort Study) by Yuliya O. Vasenyova, Irina V. Vakhlova, Oleg Yu. Averyanov

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Real-world safety profile of elexacaftor/tezacaftor/ivacaftor: a disproportionality analysis using the U.S. FDA adverse event reporting system by Chengyu Zhu, Zhiwei Cui, Tingting Liu, Siyu Lou, Linmei Zhou, Junyou Chen, Ruizhen Zhao, Li Wang, Yingyong Ou, Fan Zou

Subjects: “…CFTR modulator…”
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Optimization of ivacaftor-loaded solid lipid nanoparticles for solubility enhancement by Akshay Parihar, Akshay Parihar, Bhupendra G. Prajapati, Bhupendra G. Prajapati, Bhupendra G. Prajapati, Himanshu Paliwal

Subjects: “…CFTR modulator…”
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A Retrospective, Longitudinal Registry Study on the Long-Term Durability of Ivacaftor Treatment in People with Cystic Fibrosis by Christian Merlo, Teja Thorat, Lisa J. McGarry, Christina V. Scirica, Maral DerSarkissian, Catherine Nguyen, Yuqian M. Gu, Aruna Muthukumar, Joe Healy, Jaime L. Rubin, M. Alan Brookhart

Subjects: “…CFTR modulator…”
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The effect of modulators on lung function following inpatient treatment for CF exacerbations by Anne Stone, Meredith B. Haag, Corinne A. Muirhead, Sheila Markwardt, Kelvin D. MacDonald

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Body composition changes and clinical outcomes in pediatric cystic fibrosis during 24 months of lumacaftor ivacaftor therapy based on real-world data by Marcell Imrei, Adrienn F. Kéri, Éva Gács, Ildikó Gönczi, Melinda Meláth, Éva Kosaras, Botond Demeter, Csaba Péterfia, Klára Vass, Gyöngyi Székely, Klementina Ocskay, Andrea Párniczky

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A descriptive cohort study of pregnancy and parenthood in women with cystic fibrosis by Aleksandra Duffy, Susan Parker, Simon Williams, Kenneth Hodson, Simon Doe, Carlos Echevarria, Stephen J. Bourke

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Gallbladder sludge and microlithiasis disappearance in a cystic fibrosis patient 1 year after triple combination therapy initiation by Corrado Tagliati, Daniele Veri, Andrea Pietra, Giuseppe Lanni, Davide Battista, Marco Fogante, Giulio Argalia, Cecilia Lanza, Stefano Pantano, Francesca Collini, Maria Di Sabatino, Pietro Ripani

Subjects: “…CFTR modulators…”
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Evaluation of Complex Drug Interactions Between Elexacaftor-Tezacaftor-Ivacaftor and Statins Using Physiologically Based Pharmacokinetic Modeling by Eunjin Hong, Peter S. Chung, Adupa P. Rao, Paul M. Beringer

Subjects: “…cystic fibrosis transmembrane conductance regulator (CFTR) modulator…”
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Allergic bronchopulmonary aspergillosis as an initial manifestation of cystic fibrosis: Diagnostic and therapeutic implications in the era of CFTR modulators by Georgia Mitropoulou, MD, Zisis Balmpouzis, MD, Aurelia Oberhansli-Wavre, MD, Michael Morris, PhD, Sylvain Blanchon, MD, Alain Sauty, MD, Angela Koutsokera, MD, PhD

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Clinical Efficacy and Safety of Ivacaftor/Lumacaftor Combination in Patients with Cystic Fibrosis: International Studies Review by Nataliya Yu. Kashirskaya, Nika V. Petrova, Rena A. Zinchenko

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Mejoría de la inflamación intestinal tras tratamiento con moduladores de la proteína CFTR en pacientes con fibrosis quística by Ruth García Romero, Concepción López Cárdenes, Elena Crehuá Gaudiza, Marina Álvarez Beltrán, Mercedes Murray Hurtado, Carlos Tutau Gómez, Inés Loverdos Eseverri, Encarni Torcuato Rubio, Camila García Volpe, Enrique Salcedo Lobato, María Medina Martínez, Carmen Martin Fernández, Ana Moreno Álvarez, Ana Reyes Domínguez, David González Jiménez

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Respiratory Muscle Function in Children and Adolescents with Cystic Fibrosis in the Era of CFTR Modulator Therapies by Guillermo García-Pérez-de-Sevilla, Ángela Blanco Velasco, Thomas Yvert, Verónica Sanz-Santiago, Ana Morales Tirado, Alejandro López Neyra, Cristina de Manuel, Marta Ruiz Valbuena, Margarita Pérez-Ruiz

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Integrated Approaches to Managing Cystic Fibrosis: From Nutritional Optimization to Therapeutic Advancements by Salehe Akhondian, Saeedeh Talebi

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Glucagon-like peptide1 receptor agonist treatment of cystic fibrosis-related diabetes complicated by obesity: A cases series and literature review by Ammar Ahmed, Anvitha Ankireddypalli, Tasma Harindhanavudhi, Antoinette Moran, Amir Moheet

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A Novel LC-MS/MS Method for the Measurement of Elexacaftor, Tezacaftor and Ivacaftor in Plasma, Dried Plasma Spot (DPS) and Whole Blood in Volumetric Absorptive Microsampling (VAMS... by Federica Pigliasco, Alessia Cafaro, Sebastiano Barco, Federico Cresta, Rosaria Casciaro, Nicoletta Pedemonte, Francesca Mattioli, Carlo Castellani, Giuliana Cangemi

Subjects: “…CFTR modulators…”
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Unveiling the psychosocial impact of Elexacaftor/Tezacaftor/Ivacaftor therapy in Cystic Fibrosis patients by Marta Solís García, Adrián Peláez, Rosa Mar Gómez Punter, María Criado López, Claudia Madrid Carbajal, Julio Ancochea, Jose María Eiros Bachiller, Ana Sofía Martín Hernández, María Rodrigo-García, Marta García Clemente, Rosa Mª Girón Moreno

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Effect of CFTR modulators on glucose homeostasis in children and young adults with cystic fibrosis-related diabetes: a systematic review by Paola Giordano, Giuseppina Leonetti, Vanja Granberg, Rosa Maria Pia Casolino, Giuseppe Lassandro, Maurizio Delvecchio, Giovanna Linguiti

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A Liquid Chromatography-Tandem Mass Spectrometry Method for the Quantification of Cystic Fibrosis Drugs (Caftors) in Plasma and Its Application for Therapeutic Monitoring by Valentina D’Atri, Fabrizio Corrado, François Versace, Susana Alves Saldanha, Thomas Mercier, Monia Guidi, Paul Thoueille, Sylvain Blanchon, Angela Koutsokera, Michael Vogeser, Catia Marzolini, François Girardin, Georgia Mitropoulou, Zisis Balmpouzis, Isabelle Rochat, Alain Sauty, Laurent Arthur Decosterd, Eva Choong

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