Defective Cystic Fibrosis Transmembrane Conductance Regulator Accelerates Skeletal Muscle Aging by Impairing Autophagy/Myogenesis by Ziyi Chen, Jiankun Xu, Peijie Hu, Wanting Du, Junjiang Chen, Xiaotian Zhang, Wei Zhou, Jiayang Gao, Yuantao Zhang, Bingyang Dai, Guangshuai Nie, Jun Hu, Liangbin Zhou, Shunxiang Xu, Hisao Chang Chan, Wing‐hoi Cheung, Ye Chun Ruan, Ling Qin

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The Functional Impact of VX-770 on the Cystic Fibrosis Transmembrane Conductance Regulator Is Enduring and Increases the Constitutive Activity of This Channel in Primary Airway Epi... by Heidi J. Nick, Sarah E. Christeson, Preston E. Bratcher

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Cystic Fibrosis and Reproductive Outcomes: The Latest Insights into Fertility and Pregnancy by Weronika Małagocka, Karol Zagórski, Mateusz Kozik, Nina Skalska-Dziobek, Karolina Chybowska, Maria Naruszewicz, Przemysław Cetnarowski

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CFTR expression decreases with age in several airway cell types by Timothy E. Corcoran, Matthew J. Broerman, Corrine R. Kliment, Cecilia Lo

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A descriptive cohort study of pregnancy and parenthood in women with cystic fibrosis by Aleksandra Duffy, Susan Parker, Simon Williams, Kenneth Hodson, Simon Doe, Carlos Echevarria, Stephen J. Bourke

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Analysis of Ivacaftor drug approval for cystic fibrosis patients with gating mutations. by Nemirajaiah, S.

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CFTR对前脂肪细胞增殖和分化的影响 by 晋晨晨, 杜洁仪, 黄雪莲, 王冠蕾

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CFTR Gene Mutations and their Role in Male Infertility: A Case Study by Namrata Anjankar, Akash More, Ashish P. Anjankar, Sanket S. Mahajan, Neha Nawale

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Gallbladder sludge and microlithiasis disappearance in a cystic fibrosis patient 1 year after triple combination therapy initiation by Corrado Tagliati, Daniele Veri, Andrea Pietra, Giuseppe Lanni, Davide Battista, Marco Fogante, Giulio Argalia, Cecilia Lanza, Stefano Pantano, Francesca Collini, Maria Di Sabatino, Pietro Ripani

Subjects: “…CFTR modulators…”
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Successful Therapy over 12 Months of People with Cystic Fibrosis with Rare Non-phe508del Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Mutations with Elexacaftor/Tezac... by Tomke Sütering, Sebastian F. N. Bode, Rainald Fischer, Dorit Fabricius

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Inhibiting CFTR through inh-172 in primary neutrophils reveals CFTR-specific functional defects by Ana Lúcia Da Silva Cunha, Marfa Blanter, Janne Renders, Mieke Gouwy, Natalie Lorent, Mieke Boon, Sofie Struyf, Marianne S. Carlon

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A severe early presentation of cystic fibrosis in an infant with a homozygous c.1375_1383del CFTR variant- a case report by Abdullah Yousef, Abdullah Yousef

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Co-segregation of the c.489+3A>G variant with p.Cys1400Ter pathogenic CFTR mutation in Cyprus: prevalence and clinical implications by Panayiotis K. Yiallouros, Pinelopi Anagnostopoulou, Panayiotis Kouis, Andreas Μ. Matthaiou, Tonia Adamidi, Phivos Ioannou, George Christopoulos, Constantina Costi, Leonidas A. Phylactou, Pavlos Fanis, Vassos Neocleous

Subjects: “…CFTR gene…”
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Cystic Fibrosis assessment in infertile couples: genetic analysis trough the Next Generation Sequencing technique by Elena D’Alcamo, Giuseppe Gullo, Gaspare Cucinella, Antonino Perino, Sofia Burgio, Andrea Etrusco, Veronica Agrigento, Serena Sclafani, Florinda Listi, Aurelio Maggio, Igea Vega, Antonio Simone Laganà, Amerigo Vitagliano, Marco Noventa, Giovanni Buzzaccarini

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Improved Clinical Outcomes With Elexacaftor/Tezacaftor/Ivacaftor in Patients With Cystic Fibrosis and Advanced Lung Disease: Real‐World Evidence From an Italian Single‐Center Study... by Nicola Perrotta, Luigi Angelo Fiorito, Gianfranco Casini, Rossella Gentile, Roberta Vescovo, Alfonso Piciocchi, Roberta Lobello, Carlo Cappelli, Roberto Poscia, Giuseppe Cimino

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Allergic bronchopulmonary aspergillosis as an initial manifestation of cystic fibrosis: Diagnostic and therapeutic implications in the era of CFTR modulators by Georgia Mitropoulou, MD, Zisis Balmpouzis, MD, Aurelia Oberhansli-Wavre, MD, Michael Morris, PhD, Sylvain Blanchon, MD, Alain Sauty, MD, Angela Koutsokera, MD, PhD

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Improvement of intestinal inflammation after treatment with CFTR modulators in cystic fibrosis patients by Ruth García Romero, Concepción López Cárdenes, Elena Crehuá Gaudiza, Marina Álvarez Beltrán, Mercedes Murray Hurtado, Carlos Tutau Gómez, Inés Loverdos Eseverri, Encarni Torcuato Rubio, Camila García Volpe, Enrique Salcedo Lobato, María Medina Martínez, Carmen Martin Fernández, Ana Moreno Álvarez, Ana Reyes Domínguez, David González Jiménez, Saioa Vicente Santamaría, Ana Tabares González, Jose Ramon Gutierrez Martinez, Sara Sierra San Nicolás, Pilar Ortiz Pérez, Luis Peña Quintana

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Clinical Efficacy and Safety of Ivacaftor/Lumacaftor Combination in Patients with Cystic Fibrosis: International Studies Review by Nataliya Yu. Kashirskaya, Nika V. Petrova, Rena A. Zinchenko

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Mejoría de la inflamación intestinal tras tratamiento con moduladores de la proteína CFTR en pacientes con fibrosis quística by Ruth García Romero, Concepción López Cárdenes, Elena Crehuá Gaudiza, Marina Álvarez Beltrán, Mercedes Murray Hurtado, Carlos Tutau Gómez, Inés Loverdos Eseverri, Encarni Torcuato Rubio, Camila García Volpe, Enrique Salcedo Lobato, María Medina Martínez, Carmen Martin Fernández, Ana Moreno Álvarez, Ana Reyes Domínguez, David González Jiménez

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Progress of personalized medicine of cystic fibrosis in the times of efficient CFTR modulators by Burkhard Tümmler, Sophia Theres Pallenberg, Anna-Maria Dittrich, Simon Y. Graeber, Lutz Naehrlich, Olaf Sommerburg, Marcus A. Mall

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