Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of Literature

The Sturge-Weber syndrome (SWS) is a rare congenital disorder involving the eye in the form of glaucoma and choroidal hemangioma, facial skin in the form of port wine stain, usually in the distribution of ophthalmic division of the trigeminal nerve, and the brain in the form of leptomeningeal angiom...

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Main Authors: Mihika Dube, Rashmi Kujur, Swati Prajapati
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2017-04-01
Series:Delhi Journal of Ophthalmology
Subjects:
Online Access:https://journals.lww.com/10.7869/djo.311
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author Mihika Dube
Rashmi Kujur
Swati Prajapati
author_facet Mihika Dube
Rashmi Kujur
Swati Prajapati
author_sort Mihika Dube
collection DOAJ
description The Sturge-Weber syndrome (SWS) is a rare congenital disorder involving the eye in the form of glaucoma and choroidal hemangioma, facial skin in the form of port wine stain, usually in the distribution of ophthalmic division of the trigeminal nerve, and the brain in the form of leptomeningeal angiomas. We report a rare case of 6 year-old girl with Sturge-Weber syndrome with bilateral port wine stain involving the ophthalmic and maxillary division of trigeminal nerve, unilateral intracranial involvement, bilateral glaucoma and abnormal retinal vasculature, without the presence of choroidal hemangioma.
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institution Kabale University
issn 0972-0200
2454-2784
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publishDate 2017-04-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Delhi Journal of Ophthalmology
spelling doaj-art-ffd082bae6844adaa63813d7f85a3a082025-08-20T03:52:29ZengWolters Kluwer Medknow PublicationsDelhi Journal of Ophthalmology0972-02002454-27842017-04-01282373910.7869/djo.311Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of LiteratureMihika DubeRashmi KujurSwati PrajapatiThe Sturge-Weber syndrome (SWS) is a rare congenital disorder involving the eye in the form of glaucoma and choroidal hemangioma, facial skin in the form of port wine stain, usually in the distribution of ophthalmic division of the trigeminal nerve, and the brain in the form of leptomeningeal angiomas. We report a rare case of 6 year-old girl with Sturge-Weber syndrome with bilateral port wine stain involving the ophthalmic and maxillary division of trigeminal nerve, unilateral intracranial involvement, bilateral glaucoma and abnormal retinal vasculature, without the presence of choroidal hemangioma.https://journals.lww.com/10.7869/djo.311sturge-weber syndromeleptomeningeal angiomaport wine stainglaucomaabnormal retinal vasculature
spellingShingle Mihika Dube
Rashmi Kujur
Swati Prajapati
Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of Literature
Delhi Journal of Ophthalmology
sturge-weber syndrome
leptomeningeal angioma
port wine stain
glaucoma
abnormal retinal vasculature
title Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of Literature
title_full Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of Literature
title_fullStr Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of Literature
title_full_unstemmed Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of Literature
title_short Bilateral Ocular and Facial with Unilateral Intracranial Involvement In Sturge Weber Syndrome: A Case Report and Review of Literature
title_sort bilateral ocular and facial with unilateral intracranial involvement in sturge weber syndrome a case report and review of literature
topic sturge-weber syndrome
leptomeningeal angioma
port wine stain
glaucoma
abnormal retinal vasculature
url https://journals.lww.com/10.7869/djo.311
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AT rashmikujur bilateralocularandfacialwithunilateralintracranialinvolvementinsturgewebersyndromeacasereportandreviewofliterature
AT swatiprajapati bilateralocularandfacialwithunilateralintracranialinvolvementinsturgewebersyndromeacasereportandreviewofliterature