Waldenström Macroglobulinemia Diagnosed by Ultrasonography‐Guided Biopsy of the Right Perinephric Tumor
ABSTRACT Introduction Waldenström macroglobulinemia is a low‐grade B‐cell lymphoma characterized by lymphoplasmacytic lymphoma infiltration of the bone marrow and immunoglobulin M (IgM) protein. Case Presentation An 80s‐year‐old male presented to our hospital with chief complaints of weight loss and...
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2025-05-01
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| Online Access: | https://doi.org/10.1002/iju5.70022 |
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| author | Shingo Morinaga Shigeyuki Aoki Motoi Tobiume Genya Nishikawa Fusako Higuchi Yuusuke Ikenohata Manabu Honda Hiroe Kubo Tomoko Sawada Yoshiaki Yamada |
| author_facet | Shingo Morinaga Shigeyuki Aoki Motoi Tobiume Genya Nishikawa Fusako Higuchi Yuusuke Ikenohata Manabu Honda Hiroe Kubo Tomoko Sawada Yoshiaki Yamada |
| author_sort | Shingo Morinaga |
| collection | DOAJ |
| description | ABSTRACT Introduction Waldenström macroglobulinemia is a low‐grade B‐cell lymphoma characterized by lymphoplasmacytic lymphoma infiltration of the bone marrow and immunoglobulin M (IgM) protein. Case Presentation An 80s‐year‐old male presented to our hospital with chief complaints of weight loss and general fatigue. Computed tomography (CT) showed homogeneous tumor around the kidney with elevated soluble Interleukin‐2 receptor, serum IgM, and β2‐microglobulin levels. Histopathological analysis by ultrasonography‐guided biopsy revealed dense lymphocytic proliferation, plasmacytoid differentiation, and Dutcher bodies, positive for CD20, CD138, and IgM, but negative for CD3 and CD5, consistent with lymphoplasmacytic lymphoma. Bone marrow biopsy revealed infiltration of the lymphoplasmacytic lymphoma. The patient received four courses of bortezomib, cyclophosphamide, and dexamethasone along with dexamethasone, rituximab, and cyclophosphamide therapy. Twelve months after treatment, CT revealed only slightly enlarged abdominal para‐aortic lymph nodes. Conclusion Malignant lymphoma in perinephric lesions is a relatively rare condition; however, a definitive diagnosis can be obtained by ultrasound‐guided biopsy, allowing early initiation. |
| format | Article |
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| institution | OA Journals |
| issn | 2577-171X |
| language | English |
| publishDate | 2025-05-01 |
| publisher | Wiley |
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| series | IJU Case Reports |
| spelling | doaj-art-fecbe360f7fc4aa49e936fdf29f5ba4a2025-08-20T02:14:31ZengWileyIJU Case Reports2577-171X2025-05-018327127510.1002/iju5.70022Waldenström Macroglobulinemia Diagnosed by Ultrasonography‐Guided Biopsy of the Right Perinephric TumorShingo Morinaga0Shigeyuki Aoki1Motoi Tobiume2Genya Nishikawa3Fusako Higuchi4Yuusuke Ikenohata5Manabu Honda6Hiroe Kubo7Tomoko Sawada8Yoshiaki Yamada9Department of Urology Japan Community Health Care Organization Kani Tono Hospital Kani Gifu JapanDepartment of Urology Japan Community Health Care Organization Kani Tono Hospital Kani Gifu JapanDepartment of Urology Japan Organization of Occupational Health and Safety Asahi Rosai Hospital Owariasahi Aichi JapanDepartment of Urology Japan Organization of Occupational Health and Safety Asahi Rosai Hospital Owariasahi Aichi JapanDepartment of Clinical Laboratory Japan Community Health Care Organization Kani Tono Hospital Kani Gifu JapanDivision of Nursing Japan Community Health Care Organization Kani Tono Hospital Kani Gifu JapanDivision of Radiology Japan Community Health Care Organization Kani Tono Hospital Kani Gifu JapanDivision of Hospital and Clinic Coordination Japan Community Health Care Organization Kani Tono Hospital Kani Gifu JapanDivision of Hospital and Clinic Coordination Japan Community Health Care Organization Kani Tono Hospital Kani Gifu JapanDepartment of Urology Japan Community Health Care Organization Kani Tono Hospital Kani Gifu JapanABSTRACT Introduction Waldenström macroglobulinemia is a low‐grade B‐cell lymphoma characterized by lymphoplasmacytic lymphoma infiltration of the bone marrow and immunoglobulin M (IgM) protein. Case Presentation An 80s‐year‐old male presented to our hospital with chief complaints of weight loss and general fatigue. Computed tomography (CT) showed homogeneous tumor around the kidney with elevated soluble Interleukin‐2 receptor, serum IgM, and β2‐microglobulin levels. Histopathological analysis by ultrasonography‐guided biopsy revealed dense lymphocytic proliferation, plasmacytoid differentiation, and Dutcher bodies, positive for CD20, CD138, and IgM, but negative for CD3 and CD5, consistent with lymphoplasmacytic lymphoma. Bone marrow biopsy revealed infiltration of the lymphoplasmacytic lymphoma. The patient received four courses of bortezomib, cyclophosphamide, and dexamethasone along with dexamethasone, rituximab, and cyclophosphamide therapy. Twelve months after treatment, CT revealed only slightly enlarged abdominal para‐aortic lymph nodes. Conclusion Malignant lymphoma in perinephric lesions is a relatively rare condition; however, a definitive diagnosis can be obtained by ultrasound‐guided biopsy, allowing early initiation.https://doi.org/10.1002/iju5.70022lymphoplasmacytic lymphomamalignant lymphomaperinephric tumorultrasonography‐guided biopsyWaldenström macroglobulinemia |
| spellingShingle | Shingo Morinaga Shigeyuki Aoki Motoi Tobiume Genya Nishikawa Fusako Higuchi Yuusuke Ikenohata Manabu Honda Hiroe Kubo Tomoko Sawada Yoshiaki Yamada Waldenström Macroglobulinemia Diagnosed by Ultrasonography‐Guided Biopsy of the Right Perinephric Tumor IJU Case Reports lymphoplasmacytic lymphoma malignant lymphoma perinephric tumor ultrasonography‐guided biopsy Waldenström macroglobulinemia |
| title | Waldenström Macroglobulinemia Diagnosed by Ultrasonography‐Guided Biopsy of the Right Perinephric Tumor |
| title_full | Waldenström Macroglobulinemia Diagnosed by Ultrasonography‐Guided Biopsy of the Right Perinephric Tumor |
| title_fullStr | Waldenström Macroglobulinemia Diagnosed by Ultrasonography‐Guided Biopsy of the Right Perinephric Tumor |
| title_full_unstemmed | Waldenström Macroglobulinemia Diagnosed by Ultrasonography‐Guided Biopsy of the Right Perinephric Tumor |
| title_short | Waldenström Macroglobulinemia Diagnosed by Ultrasonography‐Guided Biopsy of the Right Perinephric Tumor |
| title_sort | waldenstrom macroglobulinemia diagnosed by ultrasonography guided biopsy of the right perinephric tumor |
| topic | lymphoplasmacytic lymphoma malignant lymphoma perinephric tumor ultrasonography‐guided biopsy Waldenström macroglobulinemia |
| url | https://doi.org/10.1002/iju5.70022 |
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