Rare Association between Minimal Change Disease and Primary Biliary Cholangitis: Case Report

Introduction: Primary biliary cholangitis (PBC) is a chronic and progressive cholestatic liver disease that is autoimmune in nature and characterized by circulating anti-mitochondrial antibodies. A wide range of autoimmune disorders have been concomitantly observed in patients with PBC, a...

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Main Authors: Neeraj Sharma, Heidi Duong, Bahman Moghadam, Tachaporn Sangwattanarat
Format: Article
Language:English
Published: Karger Publishers 2025-04-01
Series:Case Reports in Nephrology and Dialysis
Online Access:https://karger.com/article/doi/10.1159/000545015
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author Neeraj Sharma
Heidi Duong
Bahman Moghadam
Tachaporn Sangwattanarat
author_facet Neeraj Sharma
Heidi Duong
Bahman Moghadam
Tachaporn Sangwattanarat
author_sort Neeraj Sharma
collection DOAJ
description Introduction: Primary biliary cholangitis (PBC) is a chronic and progressive cholestatic liver disease that is autoimmune in nature and characterized by circulating anti-mitochondrial antibodies. A wide range of autoimmune disorders have been concomitantly observed in patients with PBC, and although quite rare PBC has been associated with a wide variety of renal disorders. Glomerular diseases have a very rare association with PBC, and these include diffuse membranous glomerulonephritis and minimal change disease, which have been sparsely described in prior literature. Presentation: Here we present a case of biopsy-proven minimal change disease in a patient with PBC treated with a course of steroids and achieving complete recovery. Conclusion: Establishing the relationship between PBC and MCD has been limited in prior literature and should be kept in mind to bring forth this rare association, which may help dictate future treatment courses.
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institution OA Journals
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publishDate 2025-04-01
publisher Karger Publishers
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series Case Reports in Nephrology and Dialysis
spelling doaj-art-fe61bc78de0b4735a2c9076d28cde6462025-08-20T02:31:56ZengKarger PublishersCase Reports in Nephrology and Dialysis2296-97052025-04-01151788210.1159/000545015Rare Association between Minimal Change Disease and Primary Biliary Cholangitis: Case ReportNeeraj SharmaHeidi DuongBahman MoghadamTachaporn Sangwattanarat Introduction: Primary biliary cholangitis (PBC) is a chronic and progressive cholestatic liver disease that is autoimmune in nature and characterized by circulating anti-mitochondrial antibodies. A wide range of autoimmune disorders have been concomitantly observed in patients with PBC, and although quite rare PBC has been associated with a wide variety of renal disorders. Glomerular diseases have a very rare association with PBC, and these include diffuse membranous glomerulonephritis and minimal change disease, which have been sparsely described in prior literature. Presentation: Here we present a case of biopsy-proven minimal change disease in a patient with PBC treated with a course of steroids and achieving complete recovery. Conclusion: Establishing the relationship between PBC and MCD has been limited in prior literature and should be kept in mind to bring forth this rare association, which may help dictate future treatment courses. https://karger.com/article/doi/10.1159/000545015
spellingShingle Neeraj Sharma
Heidi Duong
Bahman Moghadam
Tachaporn Sangwattanarat
Rare Association between Minimal Change Disease and Primary Biliary Cholangitis: Case Report
Case Reports in Nephrology and Dialysis
title Rare Association between Minimal Change Disease and Primary Biliary Cholangitis: Case Report
title_full Rare Association between Minimal Change Disease and Primary Biliary Cholangitis: Case Report
title_fullStr Rare Association between Minimal Change Disease and Primary Biliary Cholangitis: Case Report
title_full_unstemmed Rare Association between Minimal Change Disease and Primary Biliary Cholangitis: Case Report
title_short Rare Association between Minimal Change Disease and Primary Biliary Cholangitis: Case Report
title_sort rare association between minimal change disease and primary biliary cholangitis case report
url https://karger.com/article/doi/10.1159/000545015
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AT bahmanmoghadam rareassociationbetweenminimalchangediseaseandprimarybiliarycholangitiscasereport
AT tachapornsangwattanarat rareassociationbetweenminimalchangediseaseandprimarybiliarycholangitiscasereport