A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report
Vein of Galen aneurysmal malformation is a rare intracranial arteriovenous malformation, coexistence with aortic arch anomalies is even more uncommon, carry high risk of morbidity and mortality related to endovascular procedure and poor neurological outcome. Vein of Galen aneurysmal malformation is...
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Nepal Medical Association
2025-04-01
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| Series: | Journal of Nepal Medical Association |
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| Online Access: | http://www.jnma.com.np/jnma/index.php/jnma/article/view/8987 |
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| author | Krishna Deo Mandal Kalpana Subedi Unnati Amatya Janak Pathak |
| author_facet | Krishna Deo Mandal Kalpana Subedi Unnati Amatya Janak Pathak |
| author_sort | Krishna Deo Mandal |
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Vein of Galen aneurysmal malformation is a rare intracranial arteriovenous malformation, coexistence with aortic arch anomalies is even more uncommon, carry high risk of morbidity and mortality related to endovascular procedure and poor neurological outcome. Vein of Galen aneurysmal malformation is a dilated venous pouch, a persistence of the embryonic median prosencephalic vein of Markowski. Often presents with high output cardiac failure, severe pulmonary hypertension, and systemic steal leading to hemodynamic compromise and multi organ failure. Bicêtre score scale determines the potential treatment option and prognosis of the disease. Aim of the medical treatment is initial stabilization of life threatening condition of severe heart failure followed by the definitive treatment with endovascular embolization. Treatment is a big challenge, specially if coexistence with aortic arch anomalies which increases the morbidity and mortality. We describe a term neonate found to have vein of Galen aneurysmal malformation associated with bovine aortic arch.
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| format | Article |
| id | doaj-art-fd8c6e202ab14bd18bfb36ea06731bda |
| institution | Kabale University |
| issn | 0028-2715 1815-672X |
| language | English |
| publishDate | 2025-04-01 |
| publisher | Nepal Medical Association |
| record_format | Article |
| series | Journal of Nepal Medical Association |
| spelling | doaj-art-fd8c6e202ab14bd18bfb36ea06731bda2025-08-20T03:52:56ZengNepal Medical AssociationJournal of Nepal Medical Association0028-27151815-672X2025-04-016328510.31729/jnma.8987A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case ReportKrishna Deo Mandal0Kalpana Subedi1Unnati Amatya2Janak Pathak 3Department of Pediatrics and Neonatology: Paropakar Maternity and Women’s Hospital, Thapathali,Kathmandu, Nepal,Department of Pediatrics and Neonatology: Paropakar Maternity and Women’s Hospital, Thapathali,Kathmandu, Nepal,Obstetrics and Gynecology, Embassy of India, Kathmandu, NepalDepartment of Pediatrics and Neonatology: Paropakar Maternity and Women’s Hospital, Thapathali,Kathmandu, Nepal, Vein of Galen aneurysmal malformation is a rare intracranial arteriovenous malformation, coexistence with aortic arch anomalies is even more uncommon, carry high risk of morbidity and mortality related to endovascular procedure and poor neurological outcome. Vein of Galen aneurysmal malformation is a dilated venous pouch, a persistence of the embryonic median prosencephalic vein of Markowski. Often presents with high output cardiac failure, severe pulmonary hypertension, and systemic steal leading to hemodynamic compromise and multi organ failure. Bicêtre score scale determines the potential treatment option and prognosis of the disease. Aim of the medical treatment is initial stabilization of life threatening condition of severe heart failure followed by the definitive treatment with endovascular embolization. Treatment is a big challenge, specially if coexistence with aortic arch anomalies which increases the morbidity and mortality. We describe a term neonate found to have vein of Galen aneurysmal malformation associated with bovine aortic arch. http://www.jnma.com.np/jnma/index.php/jnma/article/view/8987arteriovenous malformationbovine aortic archcongenital anomaliesvein of Galen malformation |
| spellingShingle | Krishna Deo Mandal Kalpana Subedi Unnati Amatya Janak Pathak A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report Journal of Nepal Medical Association arteriovenous malformation bovine aortic arch congenital anomalies vein of Galen malformation |
| title | A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report |
| title_full | A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report |
| title_fullStr | A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report |
| title_full_unstemmed | A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report |
| title_short | A Combination Of Vein Of Galen Aneurysmal Malformation And Bovine Aortic Arch In Newborn: A Case Report |
| title_sort | combination of vein of galen aneurysmal malformation and bovine aortic arch in newborn a case report |
| topic | arteriovenous malformation bovine aortic arch congenital anomalies vein of Galen malformation |
| url | http://www.jnma.com.np/jnma/index.php/jnma/article/view/8987 |
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