Early infantile epileptic encephalopathy in the structure of microcephaly-capillary malformation syndrome: a clinical case

The article presents a clinical case of early infantile epileptic encephalopathy diagnosed in a child with a confirmed genetic study of microcephaly-capillary malformation syndrome. The extremely rare occurrence of this syndrome, as well as the small amount of information devoted to the problem of e...

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Main Authors: M. S. Maslov, A. M. Sviridova, M. A. Zalevskaya
Format: Article
Language:Russian
Published: ABV-press 2025-04-01
Series:Русский журнал детской неврологии
Subjects:
Online Access:https://rjdn.abvpress.ru/jour/article/view/510
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author M. S. Maslov
A. M. Sviridova
M. A. Zalevskaya
author_facet M. S. Maslov
A. M. Sviridova
M. A. Zalevskaya
author_sort M. S. Maslov
collection DOAJ
description The article presents a clinical case of early infantile epileptic encephalopathy diagnosed in a child with a confirmed genetic study of microcephaly-capillary malformation syndrome. The extremely rare occurrence of this syndrome, as well as the small amount of information devoted to the problem of epilepsy in this syndrome, make the presented clinical case relevant and useful for pediatric specialists (neurologists, geneticists, pediatricians). In addition, the article presents the experience of using hormone therapy in the treatment of epilepsy, which also had an effect on the main manifestation of the disease (capillary malformations).
format Article
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institution Kabale University
issn 2073-8803
2412-9178
language Russian
publishDate 2025-04-01
publisher ABV-press
record_format Article
series Русский журнал детской неврологии
spelling doaj-art-fd3ff48c40ee40f2a1dbabae8e694c902025-08-20T03:44:13ZrusABV-pressРусский журнал детской неврологии2073-88032412-91782025-04-01201323810.17650/2073-8803-2025-20-1-32-38344Early infantile epileptic encephalopathy in the structure of microcephaly-capillary malformation syndrome: a clinical caseM. S. Maslov0A. M. Sviridova1M. A. Zalevskaya2Tula Children’s Regional Clinical HospitalTula Children’s Regional Clinical HospitalTula Children’s Regional Clinical HospitalThe article presents a clinical case of early infantile epileptic encephalopathy diagnosed in a child with a confirmed genetic study of microcephaly-capillary malformation syndrome. The extremely rare occurrence of this syndrome, as well as the small amount of information devoted to the problem of epilepsy in this syndrome, make the presented clinical case relevant and useful for pediatric specialists (neurologists, geneticists, pediatricians). In addition, the article presents the experience of using hormone therapy in the treatment of epilepsy, which also had an effect on the main manifestation of the disease (capillary malformations).https://rjdn.abvpress.ru/jour/article/view/510epilepsyinfantile epilepsymicrocephaly-capillary malformation syndrome<i>stambp</i> geneearly infantile epileptic encephalopathyearly infantile myoclonic epileptic encephalopathyantiepileptic therapypharmacoresistant epilepsy
spellingShingle M. S. Maslov
A. M. Sviridova
M. A. Zalevskaya
Early infantile epileptic encephalopathy in the structure of microcephaly-capillary malformation syndrome: a clinical case
Русский журнал детской неврологии
epilepsy
infantile epilepsy
microcephaly-capillary malformation syndrome
<i>stambp</i> gene
early infantile epileptic encephalopathy
early infantile myoclonic epileptic encephalopathy
antiepileptic therapy
pharmacoresistant epilepsy
title Early infantile epileptic encephalopathy in the structure of microcephaly-capillary malformation syndrome: a clinical case
title_full Early infantile epileptic encephalopathy in the structure of microcephaly-capillary malformation syndrome: a clinical case
title_fullStr Early infantile epileptic encephalopathy in the structure of microcephaly-capillary malformation syndrome: a clinical case
title_full_unstemmed Early infantile epileptic encephalopathy in the structure of microcephaly-capillary malformation syndrome: a clinical case
title_short Early infantile epileptic encephalopathy in the structure of microcephaly-capillary malformation syndrome: a clinical case
title_sort early infantile epileptic encephalopathy in the structure of microcephaly capillary malformation syndrome a clinical case
topic epilepsy
infantile epilepsy
microcephaly-capillary malformation syndrome
<i>stambp</i> gene
early infantile epileptic encephalopathy
early infantile myoclonic epileptic encephalopathy
antiepileptic therapy
pharmacoresistant epilepsy
url https://rjdn.abvpress.ru/jour/article/view/510
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AT amsviridova earlyinfantileepilepticencephalopathyinthestructureofmicrocephalycapillarymalformationsyndromeaclinicalcase
AT mazalevskaya earlyinfantileepilepticencephalopathyinthestructureofmicrocephalycapillarymalformationsyndromeaclinicalcase