Advancing Future Amyotrophic Lateral Sclerosis Medicines by Incorporating The Patient Voice Into Patient-Centered Holistic Measurement Strategies for Clinical and Real-World Studies: Results from Targeted Literature Reviews

Abstract Introduction This analysis sought to understand the patient experience in amyotrophic lateral sclerosis (ALS) and to assess whether commonly used clinical outcome assessments (COAs) reliably and validly capture that experience. Methods Two targeted literature reviews were conducted to ident...

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Main Authors: Diana Rofail, Michael Chladek, Betsy Williams, Nick Patel, William B. Nowell, Stella Karantzoulis, Oren Levy
Format: Article
Language:English
Published: Adis, Springer Healthcare 2025-05-01
Series:Neurology and Therapy
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Online Access:https://doi.org/10.1007/s40120-025-00740-y
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author Diana Rofail
Michael Chladek
Betsy Williams
Nick Patel
William B. Nowell
Stella Karantzoulis
Oren Levy
author_facet Diana Rofail
Michael Chladek
Betsy Williams
Nick Patel
William B. Nowell
Stella Karantzoulis
Oren Levy
author_sort Diana Rofail
collection DOAJ
description Abstract Introduction This analysis sought to understand the patient experience in amyotrophic lateral sclerosis (ALS) and to assess whether commonly used clinical outcome assessments (COAs) reliably and validly capture that experience. Methods Two targeted literature reviews were conducted to identify and describe key concepts potentially important to patients (signs, symptoms, impacts), and identify commonly used COAs in ALS. Insights gained were used to map target COAs to concepts identified as potentially relevant to patients and their caregivers. COAs of interest were further examined to evaluate evidence of their validity and reliability within ALS. Results Forty-three articles were identified for concept extraction. Signs and symptoms were identified across multiple themes: motor; non-motor; respiratory; cognitive; and behavioral. Patient impacts were identified across multiple themes: physical; functional; emotional; social; and other aspects of well-being. Caregiver impacts were identified across four themes: general; emotional; social; and physical. Of 236 unique COAs identified, 6 were found to provide the greatest coverage of potentially important concepts. Closer examination of these showed some evidence gaps supporting content validity and/or psychometric properties. Conclusions Several concepts related to ALS were identified that are relevant to patients in their daily lives. We identified and reviewed COAs commonly used in assessing these concepts, and found gaps in their content validity and/or psychometric properties. These findings suggest the need for further testing/refinement of existing tools, and the opportunity to use other instruments alongside those most frequently used (e.g., ALSFRS-R) to comprehensively capture the patient experience of ALS in future clinical trial and real-world studies.
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spelling doaj-art-fb6d427a406348f08f27fe17c60c9db72025-08-20T03:46:32ZengAdis, Springer HealthcareNeurology and Therapy2193-82532193-65362025-05-011441311134310.1007/s40120-025-00740-yAdvancing Future Amyotrophic Lateral Sclerosis Medicines by Incorporating The Patient Voice Into Patient-Centered Holistic Measurement Strategies for Clinical and Real-World Studies: Results from Targeted Literature ReviewsDiana Rofail0Michael Chladek1Betsy Williams2Nick Patel3William B. Nowell4Stella Karantzoulis5Oren Levy6Regeneron Pharmaceuticals, Inc.IQVIAIQVIARegeneron Pharmaceuticals, Inc.Regeneron Pharmaceuticals, Inc.IQVIARegeneron Pharmaceuticals, Inc.Abstract Introduction This analysis sought to understand the patient experience in amyotrophic lateral sclerosis (ALS) and to assess whether commonly used clinical outcome assessments (COAs) reliably and validly capture that experience. Methods Two targeted literature reviews were conducted to identify and describe key concepts potentially important to patients (signs, symptoms, impacts), and identify commonly used COAs in ALS. Insights gained were used to map target COAs to concepts identified as potentially relevant to patients and their caregivers. COAs of interest were further examined to evaluate evidence of their validity and reliability within ALS. Results Forty-three articles were identified for concept extraction. Signs and symptoms were identified across multiple themes: motor; non-motor; respiratory; cognitive; and behavioral. Patient impacts were identified across multiple themes: physical; functional; emotional; social; and other aspects of well-being. Caregiver impacts were identified across four themes: general; emotional; social; and physical. Of 236 unique COAs identified, 6 were found to provide the greatest coverage of potentially important concepts. Closer examination of these showed some evidence gaps supporting content validity and/or psychometric properties. Conclusions Several concepts related to ALS were identified that are relevant to patients in their daily lives. We identified and reviewed COAs commonly used in assessing these concepts, and found gaps in their content validity and/or psychometric properties. These findings suggest the need for further testing/refinement of existing tools, and the opportunity to use other instruments alongside those most frequently used (e.g., ALSFRS-R) to comprehensively capture the patient experience of ALS in future clinical trial and real-world studies.https://doi.org/10.1007/s40120-025-00740-yAmyotrophic lateral sclerosisPatient experienceHumanistic impactClinical outcome assessmentsPatient-centered outcomes research
spellingShingle Diana Rofail
Michael Chladek
Betsy Williams
Nick Patel
William B. Nowell
Stella Karantzoulis
Oren Levy
Advancing Future Amyotrophic Lateral Sclerosis Medicines by Incorporating The Patient Voice Into Patient-Centered Holistic Measurement Strategies for Clinical and Real-World Studies: Results from Targeted Literature Reviews
Neurology and Therapy
Amyotrophic lateral sclerosis
Patient experience
Humanistic impact
Clinical outcome assessments
Patient-centered outcomes research
title Advancing Future Amyotrophic Lateral Sclerosis Medicines by Incorporating The Patient Voice Into Patient-Centered Holistic Measurement Strategies for Clinical and Real-World Studies: Results from Targeted Literature Reviews
title_full Advancing Future Amyotrophic Lateral Sclerosis Medicines by Incorporating The Patient Voice Into Patient-Centered Holistic Measurement Strategies for Clinical and Real-World Studies: Results from Targeted Literature Reviews
title_fullStr Advancing Future Amyotrophic Lateral Sclerosis Medicines by Incorporating The Patient Voice Into Patient-Centered Holistic Measurement Strategies for Clinical and Real-World Studies: Results from Targeted Literature Reviews
title_full_unstemmed Advancing Future Amyotrophic Lateral Sclerosis Medicines by Incorporating The Patient Voice Into Patient-Centered Holistic Measurement Strategies for Clinical and Real-World Studies: Results from Targeted Literature Reviews
title_short Advancing Future Amyotrophic Lateral Sclerosis Medicines by Incorporating The Patient Voice Into Patient-Centered Holistic Measurement Strategies for Clinical and Real-World Studies: Results from Targeted Literature Reviews
title_sort advancing future amyotrophic lateral sclerosis medicines by incorporating the patient voice into patient centered holistic measurement strategies for clinical and real world studies results from targeted literature reviews
topic Amyotrophic lateral sclerosis
Patient experience
Humanistic impact
Clinical outcome assessments
Patient-centered outcomes research
url https://doi.org/10.1007/s40120-025-00740-y
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