Polydatin-curcumin formulation alleviates CTD-ILD-like lung injury in mice via GABBR/PI3K/AKT/TGF-β pathway

Connective tissue disease-associated interstitial lung disease (CTD-ILD) is a systemic autoimmune disease with high morbidity and hazard, characterized by progressive pulmonary inflammation and fibrosis. The monomer formulation of polydatin and curcumin (PD + Cur) for lung injury in CTD-ILD was opti...

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Main Authors: Zhengju Zhang, Yao Zhang, Qingyi Lu, Yanan Wang, Guodong Li, Guoju Jin, Weiguo Ma, Yuyue Liu, Lei Yang, Hui Liu, Honghong Zhang, Wen Gu, Xinqi Deng, Chunguo Wang, Fengxian Meng
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Language:English
Published: Frontiers Media S.A. 2025-06-01
Series:Frontiers in Pharmacology
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Online Access:https://www.frontiersin.org/articles/10.3389/fphar.2025.1573525/full
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author Zhengju Zhang
Yao Zhang
Qingyi Lu
Yanan Wang
Guodong Li
Guoju Jin
Weiguo Ma
Yuyue Liu
Lei Yang
Hui Liu
Honghong Zhang
Wen Gu
Xinqi Deng
Chunguo Wang
Fengxian Meng
author_facet Zhengju Zhang
Yao Zhang
Qingyi Lu
Yanan Wang
Guodong Li
Guoju Jin
Weiguo Ma
Yuyue Liu
Lei Yang
Hui Liu
Honghong Zhang
Wen Gu
Xinqi Deng
Chunguo Wang
Fengxian Meng
author_sort Zhengju Zhang
collection DOAJ
description Connective tissue disease-associated interstitial lung disease (CTD-ILD) is a systemic autoimmune disease with high morbidity and hazard, characterized by progressive pulmonary inflammation and fibrosis. The monomer formulation of polydatin and curcumin (PD + Cur) for lung injury in CTD-ILD was optimized from Curcumae Longae Rhizoma (Curcuma Longa L.) and Polygoni Cuspidati Rhizoma Et Radix (Polygonum cuspidatum Sieb. et Zucc.). Mice with CTD-ILD-like lung injury were established by a single intratracheal drip of bleomycin. After intervening in model mice for 4 weeks, PD + Cur attenuated alveolar atrophy, fibrillar collagen formation, and thickened alveolar septa in the lung, improved serum biomarkers TOLLIP, MUC5B, KL-6, SP-D, and RCN3, and suppressed serum immunoinflammatory factors IL-6, CCL-18, and SF. The transcriptome sequencing showed that PD + Cur ameliorated CTD-ILD mainly by regulating aberrant immunoinflammation, which was further confirmed by proteomics that the PI3K/AKT/TGF-β pathway was a key pathway. Further, PD + Cur was found to affect amino acid metabolism in the serum significantly. The B-type receptor for GABA (GABBR) agonist baclofen was further found to attenuate CTD-ILD-like lung injury and modulate PI3K/AKT/TGF-β signaling. However, the inhibition of AKT, transforming growth factor beta receptor type 3 (TGFβR3), a key indicator downstream of PI3-kinase subunit p85-alpha (PI3KR1), by PD + Cur was reversed after intervention with the GABBR receptor inhibitor CGP52432. PD + Cur has an ameliorative effect on CTD-ILD-like lung injury by targeting GABBR to modulate the PI3K/AKT/TGF-β pathway.
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publisher Frontiers Media S.A.
record_format Article
series Frontiers in Pharmacology
spelling doaj-art-fb1e8f190b754c859eba0dd4e4a6de8c2025-08-20T02:03:25ZengFrontiers Media S.A.Frontiers in Pharmacology1663-98122025-06-011610.3389/fphar.2025.15735251573525Polydatin-curcumin formulation alleviates CTD-ILD-like lung injury in mice via GABBR/PI3K/AKT/TGF-β pathwayZhengju Zhang0Yao Zhang1Qingyi Lu2Yanan Wang3Guodong Li4Guoju Jin5Weiguo Ma6Yuyue Liu7Lei Yang8Hui Liu9Honghong Zhang10Wen Gu11Xinqi Deng12Chunguo Wang13Fengxian Meng14Beijing University of Chinese Medicine, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaCapital Medical University, Beijing, ChinaChangping District Hospital of Integrated Traditional Chinese and Western Medicine, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaShunyi Hospital, Beijing Traditional Chinese Medicine Hospital, Beijing, ChinaCapital Medical University, Beijing, ChinaInstitute Of Chinese Materia Medica China Academy of Chinese Medical Sciences, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaConnective tissue disease-associated interstitial lung disease (CTD-ILD) is a systemic autoimmune disease with high morbidity and hazard, characterized by progressive pulmonary inflammation and fibrosis. The monomer formulation of polydatin and curcumin (PD + Cur) for lung injury in CTD-ILD was optimized from Curcumae Longae Rhizoma (Curcuma Longa L.) and Polygoni Cuspidati Rhizoma Et Radix (Polygonum cuspidatum Sieb. et Zucc.). Mice with CTD-ILD-like lung injury were established by a single intratracheal drip of bleomycin. After intervening in model mice for 4 weeks, PD + Cur attenuated alveolar atrophy, fibrillar collagen formation, and thickened alveolar septa in the lung, improved serum biomarkers TOLLIP, MUC5B, KL-6, SP-D, and RCN3, and suppressed serum immunoinflammatory factors IL-6, CCL-18, and SF. The transcriptome sequencing showed that PD + Cur ameliorated CTD-ILD mainly by regulating aberrant immunoinflammation, which was further confirmed by proteomics that the PI3K/AKT/TGF-β pathway was a key pathway. Further, PD + Cur was found to affect amino acid metabolism in the serum significantly. The B-type receptor for GABA (GABBR) agonist baclofen was further found to attenuate CTD-ILD-like lung injury and modulate PI3K/AKT/TGF-β signaling. However, the inhibition of AKT, transforming growth factor beta receptor type 3 (TGFβR3), a key indicator downstream of PI3-kinase subunit p85-alpha (PI3KR1), by PD + Cur was reversed after intervention with the GABBR receptor inhibitor CGP52432. PD + Cur has an ameliorative effect on CTD-ILD-like lung injury by targeting GABBR to modulate the PI3K/AKT/TGF-β pathway.https://www.frontiersin.org/articles/10.3389/fphar.2025.1573525/fullCTD-ILDpolydatincurcuminGABBRPI3K/AKT/TGF-β
spellingShingle Zhengju Zhang
Yao Zhang
Qingyi Lu
Yanan Wang
Guodong Li
Guoju Jin
Weiguo Ma
Yuyue Liu
Lei Yang
Hui Liu
Honghong Zhang
Wen Gu
Xinqi Deng
Chunguo Wang
Fengxian Meng
Polydatin-curcumin formulation alleviates CTD-ILD-like lung injury in mice via GABBR/PI3K/AKT/TGF-β pathway
Frontiers in Pharmacology
CTD-ILD
polydatin
curcumin
GABBR
PI3K/AKT/TGF-β
title Polydatin-curcumin formulation alleviates CTD-ILD-like lung injury in mice via GABBR/PI3K/AKT/TGF-β pathway
title_full Polydatin-curcumin formulation alleviates CTD-ILD-like lung injury in mice via GABBR/PI3K/AKT/TGF-β pathway
title_fullStr Polydatin-curcumin formulation alleviates CTD-ILD-like lung injury in mice via GABBR/PI3K/AKT/TGF-β pathway
title_full_unstemmed Polydatin-curcumin formulation alleviates CTD-ILD-like lung injury in mice via GABBR/PI3K/AKT/TGF-β pathway
title_short Polydatin-curcumin formulation alleviates CTD-ILD-like lung injury in mice via GABBR/PI3K/AKT/TGF-β pathway
title_sort polydatin curcumin formulation alleviates ctd ild like lung injury in mice via gabbr pi3k akt tgf β pathway
topic CTD-ILD
polydatin
curcumin
GABBR
PI3K/AKT/TGF-β
url https://www.frontiersin.org/articles/10.3389/fphar.2025.1573525/full
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