MyoMed205 Counteracts Titin Hyperphosphorylation and the Expression of Contraction‐Regulating Proteins in a Rat Model of HFpEF

ABSTRACT Background Heart failure with preserved ejection fraction (HFpEF) is associated with exercise intolerance, accompanied by alterations in the peripheral skeletal muscle (SKM). We have recently shown that titin, a giant sarcomere protein, is hyperphosphorylated in HFpEF. MuRF1 is a muscle‐spe...

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Main Authors: Beatrice Vahle, Antje Schauer, Antje Augstein, Maria‐Elisa Prieto Jarabo, Janet Friedrich, Peggy Barthel, Anita Männel, Norman Mangner, Siegfried Labeit, T. Scott Bowen, Axel Linke, Volker Adams
Format: Article
Language:English
Published: Wiley 2025-06-01
Series:Journal of Cachexia, Sarcopenia and Muscle
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Online Access:https://doi.org/10.1002/jcsm.13843
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author Beatrice Vahle
Antje Schauer
Antje Augstein
Maria‐Elisa Prieto Jarabo
Janet Friedrich
Peggy Barthel
Anita Männel
Norman Mangner
Siegfried Labeit
T. Scott Bowen
Axel Linke
Volker Adams
author_facet Beatrice Vahle
Antje Schauer
Antje Augstein
Maria‐Elisa Prieto Jarabo
Janet Friedrich
Peggy Barthel
Anita Männel
Norman Mangner
Siegfried Labeit
T. Scott Bowen
Axel Linke
Volker Adams
author_sort Beatrice Vahle
collection DOAJ
description ABSTRACT Background Heart failure with preserved ejection fraction (HFpEF) is associated with exercise intolerance, accompanied by alterations in the peripheral skeletal muscle (SKM). We have recently shown that titin, a giant sarcomere protein, is hyperphosphorylated in HFpEF. MuRF1 is a muscle‐specific ubiquitin E3‐ligase that interacts with titin. Blocking this interaction via small molecules (MyoMed205) can improve muscle function and mitochondrial activity in HFpEF. This study aimed to investigate the impact of MyoMed205 on titin phosphorylation and its association with changes in muscle structure and function. Methods Obese ZSF1 rats with established HFpEF received rat chow with (n = 15) or without (n = 15) MyoMed205 and were compared with lean littermates (n = 15), serving as controls. After 12 weeks, in vitro SKM force, atrophy and titin—as well as contractile protein expression—were evaluated (soleus and extensor digitorum longus [EDL]). Statistical analysis was performed via multiple unpaired t‐test or one‐way ANOVA. Results In HFpEF, titin hyperphosphorylation by 13% in the EDL (p = 0.09) and 14% (p = 0.03) in the soleus muscle was evident. This hyperphosphorylation was driven in part by an increase in S11878 phosphorylation (EDL: +68%, p = 0.004; Sol: +23.8%, p = 0.03), which was linked to myofiber atrophy (r = −0.68, p = 0.006) and a decline in maximal specific muscle force (r = −0.54, p = 0.008). In the EDL, significant changes in protein expression related to atrophy (MuRF1 [+24.9%, p = 0.02], GDF8 [+20.6%, p = 0.09]) and calcium handling (slow troponin C [−46%, p = 0.02], fast troponin I [+35.8%, p = 0.02]) were found in HFpEF. All of the above‐mentioned effects in HFpEF were almost completely abolished by MyoMed205 treatment, and significantly elevated titin expression was visible (+19.7%, pcon = 0.04, pHFpEF = 0.01). Conclusions Titin hyperphosphorylation may negatively impact skeletal muscle integrity and function in HFpEF. MyoMed205 reduced titin hyperphosphorylation and was associated with preserved skeletal muscle function and mass. Further studies are necessary to confirm the direct role of titin hyperphosphorylation on muscle function and to evaluate the therapeutic potential of MyoMed205 in HFpEF.
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spelling doaj-art-fb1b59baee224165b8a80a883d419e492025-08-20T03:32:25ZengWileyJournal of Cachexia, Sarcopenia and Muscle2190-59912190-60092025-06-01163n/an/a10.1002/jcsm.13843MyoMed205 Counteracts Titin Hyperphosphorylation and the Expression of Contraction‐Regulating Proteins in a Rat Model of HFpEFBeatrice Vahle0Antje Schauer1Antje Augstein2Maria‐Elisa Prieto Jarabo3Janet Friedrich4Peggy Barthel5Anita Männel6Norman Mangner7Siegfried Labeit8T. Scott Bowen9Axel Linke10Volker Adams11Heart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyDZHK Partner Site Mannheim‐Heidelberg, Medical Faculty Mannheim University of Heidelberg Mannheim GermanySchool of Biomedical Sciences, Faculty of Biological Sciences University of Leeds Leeds UKHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyHeart Center, University Clinic, Department of Internal Medicine, Laboratory of Molecular and Experimental Cardiology University of Technology Dresden Dresden GermanyABSTRACT Background Heart failure with preserved ejection fraction (HFpEF) is associated with exercise intolerance, accompanied by alterations in the peripheral skeletal muscle (SKM). We have recently shown that titin, a giant sarcomere protein, is hyperphosphorylated in HFpEF. MuRF1 is a muscle‐specific ubiquitin E3‐ligase that interacts with titin. Blocking this interaction via small molecules (MyoMed205) can improve muscle function and mitochondrial activity in HFpEF. This study aimed to investigate the impact of MyoMed205 on titin phosphorylation and its association with changes in muscle structure and function. Methods Obese ZSF1 rats with established HFpEF received rat chow with (n = 15) or without (n = 15) MyoMed205 and were compared with lean littermates (n = 15), serving as controls. After 12 weeks, in vitro SKM force, atrophy and titin—as well as contractile protein expression—were evaluated (soleus and extensor digitorum longus [EDL]). Statistical analysis was performed via multiple unpaired t‐test or one‐way ANOVA. Results In HFpEF, titin hyperphosphorylation by 13% in the EDL (p = 0.09) and 14% (p = 0.03) in the soleus muscle was evident. This hyperphosphorylation was driven in part by an increase in S11878 phosphorylation (EDL: +68%, p = 0.004; Sol: +23.8%, p = 0.03), which was linked to myofiber atrophy (r = −0.68, p = 0.006) and a decline in maximal specific muscle force (r = −0.54, p = 0.008). In the EDL, significant changes in protein expression related to atrophy (MuRF1 [+24.9%, p = 0.02], GDF8 [+20.6%, p = 0.09]) and calcium handling (slow troponin C [−46%, p = 0.02], fast troponin I [+35.8%, p = 0.02]) were found in HFpEF. All of the above‐mentioned effects in HFpEF were almost completely abolished by MyoMed205 treatment, and significantly elevated titin expression was visible (+19.7%, pcon = 0.04, pHFpEF = 0.01). Conclusions Titin hyperphosphorylation may negatively impact skeletal muscle integrity and function in HFpEF. MyoMed205 reduced titin hyperphosphorylation and was associated with preserved skeletal muscle function and mass. Further studies are necessary to confirm the direct role of titin hyperphosphorylation on muscle function and to evaluate the therapeutic potential of MyoMed205 in HFpEF.https://doi.org/10.1002/jcsm.13843atrophycontractile proteinsHFpEFMuRF1MyoMed205sarcopenia
spellingShingle Beatrice Vahle
Antje Schauer
Antje Augstein
Maria‐Elisa Prieto Jarabo
Janet Friedrich
Peggy Barthel
Anita Männel
Norman Mangner
Siegfried Labeit
T. Scott Bowen
Axel Linke
Volker Adams
MyoMed205 Counteracts Titin Hyperphosphorylation and the Expression of Contraction‐Regulating Proteins in a Rat Model of HFpEF
Journal of Cachexia, Sarcopenia and Muscle
atrophy
contractile proteins
HFpEF
MuRF1
MyoMed205
sarcopenia
title MyoMed205 Counteracts Titin Hyperphosphorylation and the Expression of Contraction‐Regulating Proteins in a Rat Model of HFpEF
title_full MyoMed205 Counteracts Titin Hyperphosphorylation and the Expression of Contraction‐Regulating Proteins in a Rat Model of HFpEF
title_fullStr MyoMed205 Counteracts Titin Hyperphosphorylation and the Expression of Contraction‐Regulating Proteins in a Rat Model of HFpEF
title_full_unstemmed MyoMed205 Counteracts Titin Hyperphosphorylation and the Expression of Contraction‐Regulating Proteins in a Rat Model of HFpEF
title_short MyoMed205 Counteracts Titin Hyperphosphorylation and the Expression of Contraction‐Regulating Proteins in a Rat Model of HFpEF
title_sort myomed205 counteracts titin hyperphosphorylation and the expression of contraction regulating proteins in a rat model of hfpef
topic atrophy
contractile proteins
HFpEF
MuRF1
MyoMed205
sarcopenia
url https://doi.org/10.1002/jcsm.13843
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