A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of Literature
Hemangiomas are common tumors, accounting for 4 to 5% of all benign tumors in infancy and childhood. While they typically occur superficially, their presence in bone is extremely rare. This case report involves an 8-year-old female patient with a left scapular hemangioma, thrombocytopenia, and consu...
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| Series: | Indian Journal of Medical and Paediatric Oncology |
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| author | Rajesh Bahadur Singh Nitesh Joshi Saravana Kumar Jagannathan Raghawesh Ranjan Zachariah Chowdhury Paramita Rudra Pal |
| author_facet | Rajesh Bahadur Singh Nitesh Joshi Saravana Kumar Jagannathan Raghawesh Ranjan Zachariah Chowdhury Paramita Rudra Pal |
| author_sort | Rajesh Bahadur Singh |
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| description | Hemangiomas are common tumors, accounting for 4 to 5% of all benign tumors in infancy and childhood. While they typically occur superficially, their presence in bone is extremely rare. This case report involves an 8-year-old female patient with a left scapular hemangioma, thrombocytopenia, and consumptive coagulopathy (Kasabach–Merritt syndrome). The patient presented with a slow-growing osseous lump in the left scapular region over 3 years. Magnetic resonance imaging revealed an expansile lytic lesion originating from the left scapula, with a large soft tissue component, areas of hemorrhage, necrosis, and bony destruction. A preoperative biopsy suggested hemangioma. During evaluation, the patient was found to have a low platelet count and consumptive coagulopathy, leading to a diagnosis of Kasabach–Merritt syndrome. The patient was managed with multimodal drug therapy. Due to the large size and progression of the lesion, a total scapulectomy was performed. Postoperatively, blood parameters normalized. Final histopathology confirmed a cavernous hemangioma. No recurrence or derangement in the coagulation profile was observed at the 6-month follow-up through clinical and X-ray examinations. This report is presented due to its exceptional rarity. |
| format | Article |
| id | doaj-art-fab72b06e62b4bbba96d292e94d4b610 |
| institution | Kabale University |
| issn | 0971-5851 0975-2129 |
| language | English |
| publisher | Thieme Medical and Scientific Publishers Pvt. Ltd. |
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| series | Indian Journal of Medical and Paediatric Oncology |
| spelling | doaj-art-fab72b06e62b4bbba96d292e94d4b6102025-08-20T03:25:52ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Medical and Paediatric Oncology0971-58510975-212910.1055/s-0045-1806777A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of LiteratureRajesh Bahadur Singh0Nitesh Joshi1Saravana Kumar Jagannathan2Raghawesh Ranjan3Zachariah Chowdhury4Paramita Rudra Pal5Orthopaedic Oncosurgery Unit, Department of Surgical Oncology, Mahamana Pandit Madanmohan Malaviya Cancer Centre and Homi Bhabha Cancer Hospital, Tata Memorial Centre (Homi Bhabha National Institute), Varanasi, Uttar Pradesh, IndiaDepartment of Surgical Oncology, Mahamana Pandit Madanmohan Malaviya Cancer Centre and Homi Bhabha Cancer Hospital, Tata Memorial Centre (Homi Bhabha National Institute), Varanasi, Uttar Pradesh, IndiaOrthopaedic Oncosurgery Unit, Department of Surgical Oncology, Mahamana Pandit Madanmohan Malaviya Cancer Centre and Homi Bhabha Cancer Hospital, Tata Memorial Centre (Homi Bhabha National Institute), Varanasi, Uttar Pradesh, IndiaDepartment of Paediatric Oncology, Mahamana Pandit Madanmohan Malaviya Cancer Centre and Homi Bhabha Cancer Hospital, Tata Memorial Centre (Homi Bhabha National Institute), Varanasi, Uttar Pradesh, IndiaDepartment of Oncopathology, Mahamana Pandit Madanmohan Malaviya Cancer Centre and Homi Bhabha Cancer Hospital, Tata Memorial Centre (Homi Bhabha National Institute), Varanasi, Uttar Pradesh, IndiaDepartment of Oncopathology, Mahamana Pandit Madanmohan Malaviya Cancer Centre and Homi Bhabha Cancer Hospital, Tata Memorial Centre (Homi Bhabha National Institute), Varanasi, Uttar Pradesh, IndiaHemangiomas are common tumors, accounting for 4 to 5% of all benign tumors in infancy and childhood. While they typically occur superficially, their presence in bone is extremely rare. This case report involves an 8-year-old female patient with a left scapular hemangioma, thrombocytopenia, and consumptive coagulopathy (Kasabach–Merritt syndrome). The patient presented with a slow-growing osseous lump in the left scapular region over 3 years. Magnetic resonance imaging revealed an expansile lytic lesion originating from the left scapula, with a large soft tissue component, areas of hemorrhage, necrosis, and bony destruction. A preoperative biopsy suggested hemangioma. During evaluation, the patient was found to have a low platelet count and consumptive coagulopathy, leading to a diagnosis of Kasabach–Merritt syndrome. The patient was managed with multimodal drug therapy. Due to the large size and progression of the lesion, a total scapulectomy was performed. Postoperatively, blood parameters normalized. Final histopathology confirmed a cavernous hemangioma. No recurrence or derangement in the coagulation profile was observed at the 6-month follow-up through clinical and X-ray examinations. This report is presented due to its exceptional rarity.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0045-1806777hemangiomascapulaKasabach–Merritt syndromeconsumptive coagulopathyangio-embolization |
| spellingShingle | Rajesh Bahadur Singh Nitesh Joshi Saravana Kumar Jagannathan Raghawesh Ranjan Zachariah Chowdhury Paramita Rudra Pal A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of Literature Indian Journal of Medical and Paediatric Oncology hemangioma scapula Kasabach–Merritt syndrome consumptive coagulopathy angio-embolization |
| title | A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of Literature |
| title_full | A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of Literature |
| title_fullStr | A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of Literature |
| title_full_unstemmed | A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of Literature |
| title_short | A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of Literature |
| title_sort | case report of scapular hemangioma with kasabach merritt syndrome an insight into various treatment strategies with review of literature |
| topic | hemangioma scapula Kasabach–Merritt syndrome consumptive coagulopathy angio-embolization |
| url | http://www.thieme-connect.de/DOI/DOI?10.1055/s-0045-1806777 |
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