A Case Report of Scapular Hemangioma with Kasabach–Merritt Syndrome: An Insight into Various Treatment Strategies with Review of Literature

Hemangiomas are common tumors, accounting for 4 to 5% of all benign tumors in infancy and childhood. While they typically occur superficially, their presence in bone is extremely rare. This case report involves an 8-year-old female patient with a left scapular hemangioma, thrombocytopenia, and consu...

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Main Authors: Rajesh Bahadur Singh, Nitesh Joshi, Saravana Kumar Jagannathan, Raghawesh Ranjan, Zachariah Chowdhury, Paramita Rudra Pal
Format: Article
Language:English
Published: Thieme Medical and Scientific Publishers Pvt. Ltd.
Series:Indian Journal of Medical and Paediatric Oncology
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Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0045-1806777
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Summary:Hemangiomas are common tumors, accounting for 4 to 5% of all benign tumors in infancy and childhood. While they typically occur superficially, their presence in bone is extremely rare. This case report involves an 8-year-old female patient with a left scapular hemangioma, thrombocytopenia, and consumptive coagulopathy (Kasabach–Merritt syndrome). The patient presented with a slow-growing osseous lump in the left scapular region over 3 years. Magnetic resonance imaging revealed an expansile lytic lesion originating from the left scapula, with a large soft tissue component, areas of hemorrhage, necrosis, and bony destruction. A preoperative biopsy suggested hemangioma. During evaluation, the patient was found to have a low platelet count and consumptive coagulopathy, leading to a diagnosis of Kasabach–Merritt syndrome. The patient was managed with multimodal drug therapy. Due to the large size and progression of the lesion, a total scapulectomy was performed. Postoperatively, blood parameters normalized. Final histopathology confirmed a cavernous hemangioma. No recurrence or derangement in the coagulation profile was observed at the 6-month follow-up through clinical and X-ray examinations. This report is presented due to its exceptional rarity.
ISSN:0971-5851
0975-2129