Two cases of hereditary benign telangiectasia in Turkey: sporadic occurrence with punctate telangiectasias surrounded by anemic halos

Hereditary benign telangiectasia (HBT) is a very uncommon, genetically inherited, benign skin disorder, identified by widespread cutaneous telangiectasias. Herein, we present two sporadic cases of HBT that were admitted to the dermatology clinic for multiple punctate telangiectasias surrounde...

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Main Authors: Zennure Takcı, Özlem Tekin, Ayla Tezer
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2015-02-01
Series:The Turkish Journal of Pediatrics
Online Access:https://turkjpediatr.org/article/view/1199
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author Zennure Takcı
Özlem Tekin
Ayla Tezer
author_facet Zennure Takcı
Özlem Tekin
Ayla Tezer
author_sort Zennure Takcı
collection DOAJ
description Hereditary benign telangiectasia (HBT) is a very uncommon, genetically inherited, benign skin disorder, identified by widespread cutaneous telangiectasias. Herein, we present two sporadic cases of HBT that were admitted to the dermatology clinic for multiple punctate telangiectasias surrounded by anemic halos, favoring sun-exposed areas. These cases had no mucosal or visceral involvement and exhibited no family history of the disorder. The phenotypes of HBT are clinically and genetically heterogeneous. More clinical experience and genetic analyses are needed to understand the basis for the genetic heterogeneity and to determine genotype-phenotype correlations. We aimed to emphasize the hereditary and clinical heterogeneity of HBT by presenting two cases of HBT with punctate telangiectasias surrounded by anemic halos, with a sporadic occurrence.
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institution DOAJ
issn 0041-4301
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language English
publishDate 2015-02-01
publisher Hacettepe University Institute of Child Health
record_format Article
series The Turkish Journal of Pediatrics
spelling doaj-art-f4fca50f065d4fec9627e751a26b60592025-08-20T02:55:41ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64212015-02-01571Two cases of hereditary benign telangiectasia in Turkey: sporadic occurrence with punctate telangiectasias surrounded by anemic halosZennure Takcı0Özlem TekinAyla TezerDepartment of Dermatology, Faculty of Medicine, Gaziosmanpasa University, Tokat, Turkey. drzennure80@yahoo.com. Hereditary benign telangiectasia (HBT) is a very uncommon, genetically inherited, benign skin disorder, identified by widespread cutaneous telangiectasias. Herein, we present two sporadic cases of HBT that were admitted to the dermatology clinic for multiple punctate telangiectasias surrounded by anemic halos, favoring sun-exposed areas. These cases had no mucosal or visceral involvement and exhibited no family history of the disorder. The phenotypes of HBT are clinically and genetically heterogeneous. More clinical experience and genetic analyses are needed to understand the basis for the genetic heterogeneity and to determine genotype-phenotype correlations. We aimed to emphasize the hereditary and clinical heterogeneity of HBT by presenting two cases of HBT with punctate telangiectasias surrounded by anemic halos, with a sporadic occurrence. https://turkjpediatr.org/article/view/1199
spellingShingle Zennure Takcı
Özlem Tekin
Ayla Tezer
Two cases of hereditary benign telangiectasia in Turkey: sporadic occurrence with punctate telangiectasias surrounded by anemic halos
The Turkish Journal of Pediatrics
title Two cases of hereditary benign telangiectasia in Turkey: sporadic occurrence with punctate telangiectasias surrounded by anemic halos
title_full Two cases of hereditary benign telangiectasia in Turkey: sporadic occurrence with punctate telangiectasias surrounded by anemic halos
title_fullStr Two cases of hereditary benign telangiectasia in Turkey: sporadic occurrence with punctate telangiectasias surrounded by anemic halos
title_full_unstemmed Two cases of hereditary benign telangiectasia in Turkey: sporadic occurrence with punctate telangiectasias surrounded by anemic halos
title_short Two cases of hereditary benign telangiectasia in Turkey: sporadic occurrence with punctate telangiectasias surrounded by anemic halos
title_sort two cases of hereditary benign telangiectasia in turkey sporadic occurrence with punctate telangiectasias surrounded by anemic halos
url https://turkjpediatr.org/article/view/1199
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AT ozlemtekin twocasesofhereditarybenigntelangiectasiainturkeysporadicoccurrencewithpunctatetelangiectasiassurroundedbyanemichalos
AT aylatezer twocasesofhereditarybenigntelangiectasiainturkeysporadicoccurrencewithpunctatetelangiectasiassurroundedbyanemichalos