Paranasal Rosai-Dorfman Disease with Osseous Destruction
Rosai-Dorfman disease is a rare histiocytic proliferative disorder of unknown etiology typically characterized by cervical lymphadenopathy. Extranodal involvement often manifests in the head and neck region. We present a 10-year-old male who presented to our hospital with left epiphora from an aggre...
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| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Wiley
2017-01-01
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| Series: | Case Reports in Otolaryngology |
| Online Access: | http://dx.doi.org/10.1155/2017/1453097 |
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| _version_ | 1849469647489859584 |
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| author | Kevin Hur Changxing Liu Jeffrey A. Koempel |
| author_facet | Kevin Hur Changxing Liu Jeffrey A. Koempel |
| author_sort | Kevin Hur |
| collection | DOAJ |
| description | Rosai-Dorfman disease is a rare histiocytic proliferative disorder of unknown etiology typically characterized by cervical lymphadenopathy. Extranodal involvement often manifests in the head and neck region. We present a 10-year-old male who presented to our hospital with left epiphora from an aggressive paranasal mass invading the left orbit with osseous destruction. The mass was surgically biopsied and debulked with histopathological examination revealing Rosai-Dorfman disease. Although rarely found in the sinuses, Rosai-Dorfman disease should be considered when evaluating sinonasal masses. |
| format | Article |
| id | doaj-art-f4bf013a5bf54cedb2ef3fd715b07eeb |
| institution | Kabale University |
| issn | 2090-6765 2090-6773 |
| language | English |
| publishDate | 2017-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Otolaryngology |
| spelling | doaj-art-f4bf013a5bf54cedb2ef3fd715b07eeb2025-08-20T03:25:23ZengWileyCase Reports in Otolaryngology2090-67652090-67732017-01-01201710.1155/2017/14530971453097Paranasal Rosai-Dorfman Disease with Osseous DestructionKevin Hur0Changxing Liu1Jeffrey A. Koempel2Caruso Department of Otolaryngology, Keck School of Medicine, University of Southern California, Los Angeles, CA 90033, USACaruso Department of Otolaryngology, Keck School of Medicine, University of Southern California, Los Angeles, CA 90033, USADivision of Otolaryngology, Head and Neck Surgery, Children’s Hospital Los Angeles, Los Angeles, CA 90027, USARosai-Dorfman disease is a rare histiocytic proliferative disorder of unknown etiology typically characterized by cervical lymphadenopathy. Extranodal involvement often manifests in the head and neck region. We present a 10-year-old male who presented to our hospital with left epiphora from an aggressive paranasal mass invading the left orbit with osseous destruction. The mass was surgically biopsied and debulked with histopathological examination revealing Rosai-Dorfman disease. Although rarely found in the sinuses, Rosai-Dorfman disease should be considered when evaluating sinonasal masses.http://dx.doi.org/10.1155/2017/1453097 |
| spellingShingle | Kevin Hur Changxing Liu Jeffrey A. Koempel Paranasal Rosai-Dorfman Disease with Osseous Destruction Case Reports in Otolaryngology |
| title | Paranasal Rosai-Dorfman Disease with Osseous Destruction |
| title_full | Paranasal Rosai-Dorfman Disease with Osseous Destruction |
| title_fullStr | Paranasal Rosai-Dorfman Disease with Osseous Destruction |
| title_full_unstemmed | Paranasal Rosai-Dorfman Disease with Osseous Destruction |
| title_short | Paranasal Rosai-Dorfman Disease with Osseous Destruction |
| title_sort | paranasal rosai dorfman disease with osseous destruction |
| url | http://dx.doi.org/10.1155/2017/1453097 |
| work_keys_str_mv | AT kevinhur paranasalrosaidorfmandiseasewithosseousdestruction AT changxingliu paranasalrosaidorfmandiseasewithosseousdestruction AT jeffreyakoempel paranasalrosaidorfmandiseasewithosseousdestruction |