Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion.
Factor XI (FXI) deficiency (Rosenthal disease or hemo- philia C) is a uncommon autosomal recessive bleeding disorder. Clinical signs and symptoms of factor XI de- ficiency are generally limited; however, significant bleeding may occur following trauma or a surgical pro- cedure. We present an adolesc...
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| Language: | English |
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Pediatric Anesthesia and Critical Care Journal
2025-04-01
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| Series: | Pediatric Anesthesia and Critical Care Journal (PACCJ) |
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| Online Access: | http://www.anestesiarianimazione.com/PACCJ%202025/Perioperative%20care%20of%20an%20adolescent%20with%20factor%20XI%20deficiency%20during%20posterior%20spinal%20fusion.pdf |
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| author | G. Parizek B. Hall R. Beltran J. D. Tobias |
| author_facet | G. Parizek B. Hall R. Beltran J. D. Tobias |
| author_sort | G. Parizek |
| collection | DOAJ |
| description | Factor XI (FXI) deficiency (Rosenthal disease or hemo- philia C) is a uncommon autosomal recessive bleeding disorder. Clinical signs and symptoms of factor XI de- ficiency are generally limited; however, significant bleeding may occur following trauma or a surgical pro- cedure. We present an adolescent with factor XI defi- ciency who presented for anesthetic care during posterior spinal fusion. The processes responsible for normal blood coagulation are presented, previous reports of peri- operative care of patients with factor XI deficiency re- viewed, and suggestions for perioperative care discussed. |
| format | Article |
| id | doaj-art-f4592c50f8a445f4975cab9e835a5113 |
| institution | OA Journals |
| issn | 2281-8421 |
| language | English |
| publishDate | 2025-04-01 |
| publisher | Pediatric Anesthesia and Critical Care Journal |
| record_format | Article |
| series | Pediatric Anesthesia and Critical Care Journal (PACCJ) |
| spelling | doaj-art-f4592c50f8a445f4975cab9e835a51132025-08-20T02:20:16ZengPediatric Anesthesia and Critical Care JournalPediatric Anesthesia and Critical Care Journal (PACCJ)2281-84212025-04-01131344010.14587/paccj.2025.5Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion.G. Parizek0B. Hall1R. Beltran2J. D. Tobias3Heritage College of Osteopathic Medicine-Dublin Campus, Dublin, Ohio and Ohia University, Athens, Ohio, USADepartment of Anesthesiology & Pain Medicine, Nationwide Children’s Hospital, Columbus, Ohio, USADepartment of Anesthesiology & Pain Medicine, The Ohio State University College of Medicine, Columbus, Ohio, USADepartment of Anesthesiology & Pain Medicine, Nationwide Children’s Hospital, Columbus, Ohio, USAFactor XI (FXI) deficiency (Rosenthal disease or hemo- philia C) is a uncommon autosomal recessive bleeding disorder. Clinical signs and symptoms of factor XI de- ficiency are generally limited; however, significant bleeding may occur following trauma or a surgical pro- cedure. We present an adolescent with factor XI defi- ciency who presented for anesthetic care during posterior spinal fusion. The processes responsible for normal blood coagulation are presented, previous reports of peri- operative care of patients with factor XI deficiency re- viewed, and suggestions for perioperative care discussed.http://www.anestesiarianimazione.com/PACCJ%202025/Perioperative%20care%20of%20an%20adolescent%20with%20factor%20XI%20deficiency%20during%20posterior%20spinal%20fusion.pdfposterior spinal fusion; coagulation; factor xi; coagula- tion disturbances |
| spellingShingle | G. Parizek B. Hall R. Beltran J. D. Tobias Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion. Pediatric Anesthesia and Critical Care Journal (PACCJ) posterior spinal fusion; coagulation; factor xi; coagula- tion disturbances |
| title | Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion. |
| title_full | Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion. |
| title_fullStr | Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion. |
| title_full_unstemmed | Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion. |
| title_short | Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion. |
| title_sort | perioperative care of an adolescent with factor xi deficiency during posterior spinal fusion |
| topic | posterior spinal fusion; coagulation; factor xi; coagula- tion disturbances |
| url | http://www.anestesiarianimazione.com/PACCJ%202025/Perioperative%20care%20of%20an%20adolescent%20with%20factor%20XI%20deficiency%20during%20posterior%20spinal%20fusion.pdf |
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