Perioperative care of an adolescent with factor XI deficiency during posterior spinal fusion.
Factor XI (FXI) deficiency (Rosenthal disease or hemo- philia C) is a uncommon autosomal recessive bleeding disorder. Clinical signs and symptoms of factor XI de- ficiency are generally limited; however, significant bleeding may occur following trauma or a surgical pro- cedure. We present an adolesc...
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| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Pediatric Anesthesia and Critical Care Journal
2025-04-01
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| Series: | Pediatric Anesthesia and Critical Care Journal (PACCJ) |
| Subjects: | |
| Online Access: | http://www.anestesiarianimazione.com/PACCJ%202025/Perioperative%20care%20of%20an%20adolescent%20with%20factor%20XI%20deficiency%20during%20posterior%20spinal%20fusion.pdf |
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| Summary: | Factor XI (FXI) deficiency (Rosenthal disease or hemo- philia C) is a uncommon autosomal recessive bleeding disorder. Clinical signs and symptoms of factor XI de- ficiency are generally limited; however, significant bleeding may occur following trauma or a surgical pro- cedure. We present an adolescent with factor XI defi- ciency who presented for anesthetic care during posterior spinal fusion. The processes responsible for normal blood coagulation are presented, previous reports of peri- operative care of patients with factor XI deficiency re- viewed, and suggestions for perioperative care discussed. |
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| ISSN: | 2281-8421 |