Late vitamin K deficiency bleeding in an infant with choledochal cyst

Infantile choledochal cyst (CC) usually presents as jaundice, vomiting, acholic stools, and hepatomegaly, and it can resemble biliary atresia. Although bleeding tendency is a rare clinical presentation of CC, it can be the first symptom, especially in infants less than 12 months of age. We re...

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Main Authors: Nada Krstovski, Dragana Janic, Lidija Dokmanovic, Jelena Lazic, Predrag Rodic, Zoran Krstic
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2010-12-01
Series:The Turkish Journal of Pediatrics
Online Access:https://turkjpediatr.org/article/view/5053
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author Nada Krstovski
Dragana Janic
Lidija Dokmanovic
Jelena Lazic
Predrag Rodic
Zoran Krstic
author_facet Nada Krstovski
Dragana Janic
Lidija Dokmanovic
Jelena Lazic
Predrag Rodic
Zoran Krstic
author_sort Nada Krstovski
collection DOAJ
description Infantile choledochal cyst (CC) usually presents as jaundice, vomiting, acholic stools, and hepatomegaly, and it can resemble biliary atresia. Although bleeding tendency is a rare clinical presentation of CC, it can be the first symptom, especially in infants less than 12 months of age. We report a case of a two-month-old infant with choledochal cyst presenting as late vitamin K deficiency bleeding (VKDB). Early recognition of diseases predisposing to VKDB and immediate investigation and treatment of warning bleeds help to prevent the worst consequences. Late VKDB is often the presenting feature of a serious underlying disease that may be recognized early. The sudden onset of bleeding tendency in infants with congenital liver or biliary tract disease may suggest not only biliary atresia but also, although extremely rare, CC. Early vitamin K administration leads to rapid normalization of hemostatic parameters, which enables major liver surgery.
format Article
id doaj-art-f36cd116ea5e4256b80eeb4f44dd0179
institution DOAJ
issn 0041-4301
2791-6421
language English
publishDate 2010-12-01
publisher Hacettepe University Institute of Child Health
record_format Article
series The Turkish Journal of Pediatrics
spelling doaj-art-f36cd116ea5e4256b80eeb4f44dd01792025-08-20T03:01:15ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64212010-12-01526Late vitamin K deficiency bleeding in an infant with choledochal cystNada Krstovski0Dragana JanicLidija DokmanovicJelena LazicPredrag RodicZoran KrsticDepartment of Pediatric Hematology, University Children's Hospital, Belgrade, Serbia. Infantile choledochal cyst (CC) usually presents as jaundice, vomiting, acholic stools, and hepatomegaly, and it can resemble biliary atresia. Although bleeding tendency is a rare clinical presentation of CC, it can be the first symptom, especially in infants less than 12 months of age. We report a case of a two-month-old infant with choledochal cyst presenting as late vitamin K deficiency bleeding (VKDB). Early recognition of diseases predisposing to VKDB and immediate investigation and treatment of warning bleeds help to prevent the worst consequences. Late VKDB is often the presenting feature of a serious underlying disease that may be recognized early. The sudden onset of bleeding tendency in infants with congenital liver or biliary tract disease may suggest not only biliary atresia but also, although extremely rare, CC. Early vitamin K administration leads to rapid normalization of hemostatic parameters, which enables major liver surgery. https://turkjpediatr.org/article/view/5053
spellingShingle Nada Krstovski
Dragana Janic
Lidija Dokmanovic
Jelena Lazic
Predrag Rodic
Zoran Krstic
Late vitamin K deficiency bleeding in an infant with choledochal cyst
The Turkish Journal of Pediatrics
title Late vitamin K deficiency bleeding in an infant with choledochal cyst
title_full Late vitamin K deficiency bleeding in an infant with choledochal cyst
title_fullStr Late vitamin K deficiency bleeding in an infant with choledochal cyst
title_full_unstemmed Late vitamin K deficiency bleeding in an infant with choledochal cyst
title_short Late vitamin K deficiency bleeding in an infant with choledochal cyst
title_sort late vitamin k deficiency bleeding in an infant with choledochal cyst
url https://turkjpediatr.org/article/view/5053
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AT draganajanic latevitaminkdeficiencybleedinginaninfantwithcholedochalcyst
AT lidijadokmanovic latevitaminkdeficiencybleedinginaninfantwithcholedochalcyst
AT jelenalazic latevitaminkdeficiencybleedinginaninfantwithcholedochalcyst
AT predragrodic latevitaminkdeficiencybleedinginaninfantwithcholedochalcyst
AT zorankrstic latevitaminkdeficiencybleedinginaninfantwithcholedochalcyst