An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and Urethra
Granulomatosis with polyangiitis (GPA) is a systemic necrotizing granulomatosis vasculitis characterized by predilection to affect small- and medium-sized blood vessels and commonly affects the upper and lower respiratory tract and kidneys in most cases. Genital involvement is reported in <1% of...
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| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Wiley
2017-01-01
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| Series: | Case Reports in Rheumatology |
| Online Access: | http://dx.doi.org/10.1155/2017/9407675 |
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| author | Sandra Soro Marín Enrique Júdez Navarro Manuela Sianes Fernández Ginés Sánchez Nievas Juan Gabriel Lorenzo Romero |
| author_facet | Sandra Soro Marín Enrique Júdez Navarro Manuela Sianes Fernández Ginés Sánchez Nievas Juan Gabriel Lorenzo Romero |
| author_sort | Sandra Soro Marín |
| collection | DOAJ |
| description | Granulomatosis with polyangiitis (GPA) is a systemic necrotizing granulomatosis vasculitis characterized by predilection to affect small- and medium-sized blood vessels and commonly affects the upper and lower respiratory tract and kidneys in most cases. Genital involvement is reported in <1% of cases in large cohorts and nearly all cases have been in the setting of multisystemic disease or during the course of the disease in patients already diagnosed as GPA. A case is presented of uncommon limited urogenital GPA in a 66-year-old woman with an irregular mass occupying urethra and vagina. The patient showed a good response after Corticoids and Methotrexate. |
| format | Article |
| id | doaj-art-f2fdf76e379b42fe9a4eb3debafbb79d |
| institution | Kabale University |
| issn | 2090-6889 2090-6897 |
| language | English |
| publishDate | 2017-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Rheumatology |
| spelling | doaj-art-f2fdf76e379b42fe9a4eb3debafbb79d2025-02-03T01:11:21ZengWileyCase Reports in Rheumatology2090-68892090-68972017-01-01201710.1155/2017/94076759407675An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and UrethraSandra Soro Marín0Enrique Júdez Navarro1Manuela Sianes Fernández2Ginés Sánchez Nievas3Juan Gabriel Lorenzo Romero4Rheumatology Unit, Hospital General de Villarrobledo, Villarrobledo, Albacete, SpainDepartment of Rheumatology, Complejo Hospitalario Universitario de Albacete, Albacete, SpainDepartment of Rheumatology, Complejo Hospitalario Universitario de Albacete, Albacete, SpainDepartment of Rheumatology, Complejo Hospitalario Universitario de Albacete, Albacete, SpainDepartment of Urology, Complejo Hospitalario Universitario de Albacete, Albacete, SpainGranulomatosis with polyangiitis (GPA) is a systemic necrotizing granulomatosis vasculitis characterized by predilection to affect small- and medium-sized blood vessels and commonly affects the upper and lower respiratory tract and kidneys in most cases. Genital involvement is reported in <1% of cases in large cohorts and nearly all cases have been in the setting of multisystemic disease or during the course of the disease in patients already diagnosed as GPA. A case is presented of uncommon limited urogenital GPA in a 66-year-old woman with an irregular mass occupying urethra and vagina. The patient showed a good response after Corticoids and Methotrexate.http://dx.doi.org/10.1155/2017/9407675 |
| spellingShingle | Sandra Soro Marín Enrique Júdez Navarro Manuela Sianes Fernández Ginés Sánchez Nievas Juan Gabriel Lorenzo Romero An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and Urethra Case Reports in Rheumatology |
| title | An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and Urethra |
| title_full | An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and Urethra |
| title_fullStr | An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and Urethra |
| title_full_unstemmed | An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and Urethra |
| title_short | An Unusual Presentation of Limited Granulomatosis with Polyangiitis Involving Vagina and Urethra |
| title_sort | unusual presentation of limited granulomatosis with polyangiitis involving vagina and urethra |
| url | http://dx.doi.org/10.1155/2017/9407675 |
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