The late diagnosis of double cortex syndrome in a 36-year-old woman with resistant atonic seizures

Subcortical laminar heterotopia (double cortex syndrome) is an orphan disease with an incidence of 1 to 200,000 people in the population. The cause of the disease is mutation of the gene DCX (synonyms: DBCN, XLIS) in chromosome Xq22.3-q23. The type of inheritance is X-linked dominant. Correct diagno...

Full description

Saved in:
Bibliographic Details
Main Authors: N. A. Shnayder, D. V. Dmitrenko, Yu. B. Govorina, E. A. Kantimirova, O. V. Alekseeva, A. A. Molgachev, A. A. Makarkin
Format: Article
Language:Russian
Published: IMA-PRESS LLC 2015-10-01
Series:Неврология, нейропсихиатрия, психосоматика
Subjects:
Online Access:https://nnp.ima-press.net/nnp/article/view/529
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850186797679640576
author N. A. Shnayder
D. V. Dmitrenko
Yu. B. Govorina
E. A. Kantimirova
O. V. Alekseeva
A. A. Molgachev
A. A. Makarkin
author_facet N. A. Shnayder
D. V. Dmitrenko
Yu. B. Govorina
E. A. Kantimirova
O. V. Alekseeva
A. A. Molgachev
A. A. Makarkin
author_sort N. A. Shnayder
collection DOAJ
description Subcortical laminar heterotopia (double cortex syndrome) is an orphan disease with an incidence of 1 to 200,000 people in the population. The cause of the disease is mutation of the gene DCX (synonyms: DBCN, XLIS) in chromosome Xq22.3-q23. The type of inheritance is X-linked dominant. Correct diagnosis requires a high degree of skills of a neurologist/epileptologist and a radiologist. The paper describes a clinical case of the late diagnosis of double cortex syndrome in a 36-year-old woman with a long history of resistant atonic seizures and mental retardation.
format Article
id doaj-art-f091b0f00a9e42749e917dfda5c5174c
institution OA Journals
issn 2074-2711
2310-1342
language Russian
publishDate 2015-10-01
publisher IMA-PRESS LLC
record_format Article
series Неврология, нейропсихиатрия, психосоматика
spelling doaj-art-f091b0f00a9e42749e917dfda5c5174c2025-08-20T02:16:14ZrusIMA-PRESS LLCНеврология, нейропсихиатрия, психосоматика2074-27112310-13422015-10-0173404510.14412/2074-2711-2015-3-40-45499The late diagnosis of double cortex syndrome in a 36-year-old woman with resistant atonic seizuresN. A. Shnayder0D. V. Dmitrenko1Yu. B. Govorina2E. A. Kantimirova3O. V. Alekseeva4A. A. Molgachev5A. A. Makarkin6Prof. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of RussiaProf. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of RussiaProf. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of RussiaProf. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of RussiaProf. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of RussiaMedical Diagnostic Centre, S.M. Berezin International Institute of Biological SystemsMedical Diagnostic Centre, S.M. Berezin International Institute of Biological SystemsSubcortical laminar heterotopia (double cortex syndrome) is an orphan disease with an incidence of 1 to 200,000 people in the population. The cause of the disease is mutation of the gene DCX (synonyms: DBCN, XLIS) in chromosome Xq22.3-q23. The type of inheritance is X-linked dominant. Correct diagnosis requires a high degree of skills of a neurologist/epileptologist and a radiologist. The paper describes a clinical case of the late diagnosis of double cortex syndrome in a 36-year-old woman with a long history of resistant atonic seizures and mental retardation.https://nnp.ima-press.net/nnp/article/view/529epilepsyatonic seizuresdifferential diagnosisdouble cortex syndromesubcortical laminar heterotopia
spellingShingle N. A. Shnayder
D. V. Dmitrenko
Yu. B. Govorina
E. A. Kantimirova
O. V. Alekseeva
A. A. Molgachev
A. A. Makarkin
The late diagnosis of double cortex syndrome in a 36-year-old woman with resistant atonic seizures
Неврология, нейропсихиатрия, психосоматика
epilepsy
atonic seizures
differential diagnosis
double cortex syndrome
subcortical laminar heterotopia
title The late diagnosis of double cortex syndrome in a 36-year-old woman with resistant atonic seizures
title_full The late diagnosis of double cortex syndrome in a 36-year-old woman with resistant atonic seizures
title_fullStr The late diagnosis of double cortex syndrome in a 36-year-old woman with resistant atonic seizures
title_full_unstemmed The late diagnosis of double cortex syndrome in a 36-year-old woman with resistant atonic seizures
title_short The late diagnosis of double cortex syndrome in a 36-year-old woman with resistant atonic seizures
title_sort late diagnosis of double cortex syndrome in a 36 year old woman with resistant atonic seizures
topic epilepsy
atonic seizures
differential diagnosis
double cortex syndrome
subcortical laminar heterotopia
url https://nnp.ima-press.net/nnp/article/view/529
work_keys_str_mv AT nashnayder thelatediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT dvdmitrenko thelatediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT yubgovorina thelatediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT eakantimirova thelatediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT ovalekseeva thelatediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT aamolgachev thelatediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT aamakarkin thelatediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT nashnayder latediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT dvdmitrenko latediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT yubgovorina latediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT eakantimirova latediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT ovalekseeva latediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT aamolgachev latediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures
AT aamakarkin latediagnosisofdoublecortexsyndromeina36yearoldwomanwithresistantatonicseizures