Kearns Sayre Syndrome: A Rare Cause of Mitochondrial Diabetes and Hypogonadotropic Hypogonadism

Kearns-Sayre syndrome is a rare mitochondrial disease that presents before the age of 20 years with ptosis, external ophthalmoplegia, and pigmentary retinopathy associated with endocrine and cardiac conduction abnormalities. Here we report an 18-year-old female presenting with fever, cough, seconda...

Full description

Saved in:
Bibliographic Details
Main Authors: Sriram Mudraje, Jaideep Khare, Nancy Garg, Sushil Jindal
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2025-02-01
Series:Case Reports in Clinical Practice
Subjects:
Online Access:https://crcp.tums.ac.ir/index.php/crcp/article/view/1010
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Kearns-Sayre syndrome is a rare mitochondrial disease that presents before the age of 20 years with ptosis, external ophthalmoplegia, and pigmentary retinopathy associated with endocrine and cardiac conduction abnormalities. Here we report an 18-year-old female presenting with fever, cough, secondary amenorrhea, diabetes ptosis, external ophthalmople gia, and ataxia . Fundosc opy revealed pigmen tary retinopathy. ECG showed intraventricular conduction abnormalities, and 2D echocardiography revealed global left ventricular hypokinesia with reduced ejection fraction. Hence, the diagnosis of Kearns-Sayre syndrome was made.
ISSN:2538-2683
2538-2691