Breathing With Half a Pulmonary Circuit: Three Cases of Unilateral Pulmonary Artery Agenesis
ABSTRACT Unilateral pulmonary artery atresia (UPAA) is a rare congenital anomaly marked by the absence of one of the pulmonary arteries. This article examines three instances of UPAA, predominantly affecting the right side, although one case involved the left side. Common characteristics included he...
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| Format: | Article |
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Wiley
2025-07-01
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| Series: | Respirology Case Reports |
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| Online Access: | https://doi.org/10.1002/rcr2.70280 |
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| author | Vignesh Kumar Kathiresan Benjamin Earnest Williams V. S. Aswith Chowdary Jonnalagadda |
| author_facet | Vignesh Kumar Kathiresan Benjamin Earnest Williams V. S. Aswith Chowdary Jonnalagadda |
| author_sort | Vignesh Kumar Kathiresan |
| collection | DOAJ |
| description | ABSTRACT Unilateral pulmonary artery atresia (UPAA) is a rare congenital anomaly marked by the absence of one of the pulmonary arteries. This article examines three instances of UPAA, predominantly affecting the right side, although one case involved the left side. Common characteristics included hemoptysis, observed in two patients—one with a chronic history necessitating embolization and another with a mild, recent onset. The third case was identified incidentally during a preoperative evaluation. All cases demonstrated varying degrees of ipsilateral lung volume reduction and associated interstitial changes or fibrosis. UPAA can be asymptomatic or present with hemoptysis, recurrent infections, or breathlessness. Diagnosis relies on computed tomography pulmonary angiography (CTPA) or magnetic resonance (MR) angiography. Management ranges from observation to embolization or pneumonectomy in severe cases. Mortality is around 7%, with pulmonary hypertension and haemorrhage being major prognostic factors. |
| format | Article |
| id | doaj-art-eda33110491f4cd0b8bef75d4bfb186a |
| institution | Kabale University |
| issn | 2051-3380 |
| language | English |
| publishDate | 2025-07-01 |
| publisher | Wiley |
| record_format | Article |
| series | Respirology Case Reports |
| spelling | doaj-art-eda33110491f4cd0b8bef75d4bfb186a2025-08-20T03:58:40ZengWileyRespirology Case Reports2051-33802025-07-01137n/an/a10.1002/rcr2.70280Breathing With Half a Pulmonary Circuit: Three Cases of Unilateral Pulmonary Artery AgenesisVignesh Kumar Kathiresan0Benjamin Earnest Williams1V. S. Aswith Chowdary Jonnalagadda2Department of Pulmonary Medicine Christian Medical College Vellore Ranipet Campus IndiaDepartment of Pulmonary Medicine Christian Medical College Vellore Ranipet Campus IndiaDepartment of Pulmonary Medicine Christian Medical College Vellore Ranipet Campus IndiaABSTRACT Unilateral pulmonary artery atresia (UPAA) is a rare congenital anomaly marked by the absence of one of the pulmonary arteries. This article examines three instances of UPAA, predominantly affecting the right side, although one case involved the left side. Common characteristics included hemoptysis, observed in two patients—one with a chronic history necessitating embolization and another with a mild, recent onset. The third case was identified incidentally during a preoperative evaluation. All cases demonstrated varying degrees of ipsilateral lung volume reduction and associated interstitial changes or fibrosis. UPAA can be asymptomatic or present with hemoptysis, recurrent infections, or breathlessness. Diagnosis relies on computed tomography pulmonary angiography (CTPA) or magnetic resonance (MR) angiography. Management ranges from observation to embolization or pneumonectomy in severe cases. Mortality is around 7%, with pulmonary hypertension and haemorrhage being major prognostic factors.https://doi.org/10.1002/rcr2.70280agenesiscollateral circulationhemoptysispulmonary arteryunilateral lung hypoplasia |
| spellingShingle | Vignesh Kumar Kathiresan Benjamin Earnest Williams V. S. Aswith Chowdary Jonnalagadda Breathing With Half a Pulmonary Circuit: Three Cases of Unilateral Pulmonary Artery Agenesis Respirology Case Reports agenesis collateral circulation hemoptysis pulmonary artery unilateral lung hypoplasia |
| title | Breathing With Half a Pulmonary Circuit: Three Cases of Unilateral Pulmonary Artery Agenesis |
| title_full | Breathing With Half a Pulmonary Circuit: Three Cases of Unilateral Pulmonary Artery Agenesis |
| title_fullStr | Breathing With Half a Pulmonary Circuit: Three Cases of Unilateral Pulmonary Artery Agenesis |
| title_full_unstemmed | Breathing With Half a Pulmonary Circuit: Three Cases of Unilateral Pulmonary Artery Agenesis |
| title_short | Breathing With Half a Pulmonary Circuit: Three Cases of Unilateral Pulmonary Artery Agenesis |
| title_sort | breathing with half a pulmonary circuit three cases of unilateral pulmonary artery agenesis |
| topic | agenesis collateral circulation hemoptysis pulmonary artery unilateral lung hypoplasia |
| url | https://doi.org/10.1002/rcr2.70280 |
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